供货周期: | 一周 |
品牌: | EterLife |
规格: | 0.1ml/100μg 、0.2ml/200μg |
货号: | TE-KT-0160 |
CAS号: | 详见产品说明书 |
酰基辅酶A脱氢酶很长链抗体
〖别名〗ACAD 6; ACAD6; ACADV_HUMAN; Acadvl; Acyl CoA dehydrogenase very long chain; Acyl Coenzyme A dehydrogenase very long chain; LCACD; mitochondrial; Very long chain specific acyl CoA dehydrogenase; Very long chain specific acyl CoA dehydrogenase mitochondrial; Very long-chain specific acyl-CoA dehydrogenase; VLCAD.
〖浓度〗1mg/1ml
〖规格〗酰基辅酶A脱氢酶很长链抗体0.2ml/200μg
〖抗体来源〗Rabbit
〖克隆类型〗polyclonal
〖交叉反应〗Human, Mouse, Rat, Dog, Pig, Cow, Horse, Rabbit
〖产品类型〗一抗
〖研究领域〗肿瘤 心血管 细胞生物 免疫学 信号转导 新陈代谢
〖蛋白分子量〗predicted molecular weight: 66kDa
〖性状〗Lyophilized or Liquid
〖免疫原〗KLH conjugated synthetic peptide derived from human ACADVL
〖亚型〗IgG
〖纯化方法〗affinity purified by Protein A
〖储存液〗0.01M PBS, pH 7.4 with 10 mg/ml BSA and 0.1% Sodium azide
〖产品应用〗WB=1:100-500 ELISA=1:500-1000 IP=1:20-100 IHC-P=1:100-500 IHC-F=1:100-500 IF=1:100-500
(石蜡切片需做抗原修复)
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
〖保存条件〗Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
Important Note This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
〖产品介绍〗ACADVL (acyl-Coenzyme A dehydrogenase, very long chain) catalyzes the first step of the mitochondrial fatty acid beta-oxidation pathway. It is specific to esters of long-chain and very long chain fatty acids such as palmitoyl-CoA and stearoyl-CoA. Deficiencies in ACADVL are associated with reduced myocardial fatty acid beta-oxidation and cardiomyopathy.
Function : Active toward esters of long-chain and very long chain fatty acids such as palmitoyl-CoA, mysritoyl-CoA and stearoyl-CoA. Can accommodate substrate acyl chain lengths as long as 24 carbons, but shows little activity for substrates of less than 12 carbons.
Subunit : Homodimer.
Subcellular Location : Mitochondrion inner membrane.
DISEASE : Defects in ACADVL are the cause of acyl-CoA dehydrogenase very long chain deficiency (ACADVLD) [MIM:201475]. ACADVLD is an autosomal recessive disease which leads to impaired long-chain fatty acid beta-oxidation. It is clinically heterogeneous, with three major phenotypes: a severe childhood form, with early onset, high mortality, and high incidence of cardiomyopathy; a milder childhood form, with later onset, usually with hypoketotic hypoglycemia as the main presenting feature, low mortality, and rare cardiomyopathy; and an adult form, with isolated skeletal muscle involvement, rhabdomyolysis, and myoglobinuria, usually triggered by exercise or fasting.
Similarity : Belongs to the acyl-CoA dehydrogenase family.
Database links : UniProtKB/Swiss-Prot: P49748.1
本公司产品现货供应,货期短,质量可靠。仅用于科研实验不应用于临床。我们用专业的态度,一流的服务,全程实验指导,让你的数据不在成为实验奇谈。选择优质的酰基辅酶A脱氢酶很长链抗体,你的小伙伴都会惊呆的。本公司专业供应各种进口、国产一抗及二抗。代理品牌有R&D、Santa Cruz、Bipec、Millipore等国际知名品牌,品种多达7000多种。让你的科研之路不再布满荆棘。
我们还可以为客户提供产品说明书。酰基辅酶A脱氢酶很长链抗体拥有高纯度、高效价、高特异性的特点,可以应用于多种实验。免费送货上门,为您大大节省了时间和金钱。
Ab-(001)-07833 CD10/CALLA (Neutral Endopeptidase) CD10抗原 ,英文名: CD10/CALLA ,规格: 0.5mg
Ab-(001)-07834 ZCWCC1(Zinc finger CW-type coiled-coil domain protein 1) ZCWCC1抗原 ,英文名: ZCWCC1 ,规格: 0.5mg
Ab-(001)-07835 CD105/Endoglin/TGF- Beta receptor CD105/转化生长因子β受体抗原 ,英文名: CD105/Endoglin/TGF- ,规格: 0.5mg
Ab-(001)-07836 CD138/Syndecan-1 多配体蛋白聚糖1抗原 ,英文名: CD138/Syndecan-1 ,规格: 0.5mg
Ab-(001)-07837 CD146/MCAM 黑色素瘤细胞粘附分子CD146抗原 ,英文名: CD146/MCAM ,规格: 0.5mg
Ab-(001)-07838 ANPEN/CD13(Aminopeptidase N) 氨肽酶N抗原 ,英文名: ANPEN/CD13 ,规格: 0.5mg
Ab-(001)-07839 CD14(cluster of differentiation antigen 14) CD14/内毒素受体抗原 ,英文名: CD14 ,规格: 0.5mg
Ab-(001)-07840 CD28 CD28抗原 ,英文名: CD28 ,规格: 0.5mg
Ab-(001)-07841 CD166/ALCAM(activated leukocyte celladhesion molecule) 活化白细胞粘附分子抗原 ,英文名: CD166/ALCAM ,规格: 0.5mg
Ab-(001)-07842 CD177/NB1 peptide 嗜中性粒细胞抗原CD177抗原 ,英文名: CD177/NB1 ,规格: 0.5mg
Ab-(001)-07843 CD24 CD24抗原 ,英文名: CD24 ,规格: 0.5mg
Ab-(001)-07844 CD24 CD24抗原 ,英文名: CD24 ,规格: 0.5mg
Ab-(001)-07845 CD2AP (CD2-associated protein) 白细胞分化抗原CD2AP ,英文名: CD2AP ,规格: 0.5mg
Ab-(001)-07846 CD33 peptide(human) CD33抗原(人) ,英文名: CD33 ,规格: 0.5mg
Ab-(001)-07847 CD33/Siglec-3(mouse ret) CD33抗原(大、小鼠) ,英文名: CD33/Siglec-3 ,规格: 0.5mg
Ab-(001)-07848 CD34 CD34抗原(细胞表面的唾液粘蛋白) ,英文名: CD34 ,规格: 0.5mg
Ab-(001)-07849 CD38(mouse, rat) CD38多肽(小鼠、大鼠) ,英文名: CD38 ,规格: 0.5mg
Ab-(001)-07850 CD38(human) CD38抗原(人) ,英文名: CD38 ,规格: 0.5mg
Ab-(001)-07851 CD36 CD36(多肽) ,英文名: CD36 ,规格: 0.5mg
Ab-(001)-07852 CD7 CD7抗原 ,英文名: CD7 ,规格: 0.5mg
Ab-(001)-07853 CD40L(CD40 Ligand/TNFSF5/CD154) CD40L抗原 ,英文名: CD40L ,规格: 0.5mg
Ab-(001)-07854 CD44 CD44抗原 (多肽抗原) ,英文名: CD44 ,规格: 0.5mg
Ab-(001)-07855 Argireline peptide 抗皱寡肽-1/六胜肽-3/阿基瑞林/乙酰六胜肽-3 ,英文名: Argireline ,规格: 1g
Ab-(001)-07856 GHRP-2 Acetate peptide(Growth hormone-releasing peptides 2) 醋酸促生长激素释放肽2 ,英文名: GHRP-2 ,规格: 1g
Ab-(001)-07857 GHRP-6 Acetate peptide(Growth hormone-releasing peptides 6) 醋酸促生长激素释放肽6 ,英文名: GHRP-6 ,规格: 1g
Ab-(001)-07858 Matrixyl Acetate 五胜肽/美容肽—M肽 ,英文名: Matrixyl ,规格: 1g
Ab-(001)-07859 MT-II(Melanotan II Acetate) 醋酸美拉诺坦II ,英文名: MT-II ,规格: 1g
Ab-(001)-07860 Pentapeptide-3/Leuphasyl 五胜肽 ,英文名: Pentapeptide-3/Leuphasyl ,规格: 1g
Ab-(001)-07861 PT141(Bremelanotide PT-141) 雌性激素肽 ,英文名: PT141 ,规格: 1g
Ab-(001)-07862 CD45(LCA/gp180) CD45抗原(白细胞共同抗原) ,英文名: CD45 ,规格: 0.5mg
Ab-(001)-07863 CD46/MCP(membrane cofactor protein)rat, mouse 膜辅蛋白/内源性辅助因子活性蛋白抗原 ,英文名: CD46/MCP ,规格: 0.5mg
Ab-(001)-07864 CD5 CD5 多肽抗原 ,英文名: CD5 ,规格: 0.5mg
Ab-(001)-07865 ICAM-2/CD102(intercellular adhesion molecules-2) 细胞间粘附分子-2抗原 ,英文名: ICAM-2/CD102 ,规格: 0.5mg
Ab-(001)-07866 CD56/NCAM1(Neural Cell Adhesion Molecule 1) 神经细胞粘附分子1抗原 ,英文名: CD56/NCAM1 ,规格: 0.5mg
Ab-(001)-07867 CD62L (ELAM-1/L-Selectin ) L选择素抗原 ,英文名: CD62L ,规格: 0.5mg
Ab-(001)-07868 E-Selectin E选择素抗原 ,英文名: E-Selectin ,规格: 0.5mg
Ab-(001)-07869 CD80/B7-1(human) 人刺激分子B7-1蛋白抗原 ,英文名: CD80/B7-1 ,规格: 0.5mg
Ab-(001)-07870 CD80/B7-1 刺激分子B7-1蛋白抗原 ,英文名: CD80/B7-1 ,规格: 0.5mg
Ab-(001)-07871 CD82/KAI1 peptide 肿瘤转移抑制蛋白1抗原 ,英文名: CD82/KAI1 ,规格: 0.5mg
Ab-(001)-07872 CD86/B7-2 CD86抗原 ,英文名: CD86/B7-2 ,规格: 0.5mg
Ab-(001)-07873 Cdc2/P34CDC2/CDK1(Cell division control protein 2) 周期素依赖激酶1抗原 ,英文名: Cdc2/P34CDC2/CDK1 ,规格: 0.5mg
Ab-(001)-07874 CD339/Jagged1 CD339/Jagged1抗原 ,英文名: CD339/Jagged1 ,规格: 0.5mg
Ab-(001)-07875 Cdc34 peptide 细胞周期调控因子34抗原 ,英文名: Cdc34 ,规格: 0.5mg
Ab-(001)-07876 CDK1 (Cyclin-Dependent Kinase 1) 周期素依赖性激酶1抗原 ,英文名: CDK1 ,酰基辅酶A脱氢酶很长链抗体规格: 0.5mg
Ab-(001)-07877 CDK5(Cyclin Dependent Kinase 5) 周期素依赖性激酶5抗原 ,英文名: CDK5 ,规格: 0.5mg
Ab-(001)-07878 CDK6 (Cyclin Dependent Kinase 6) 周期素依赖性激酶6抗原 ,英文名: CDK6 ,规格: 0.5mg
相关产品
详细地址
关注
拨打电话
留言咨询