产品详情
英文名称 EPM2AIP1
中文名称 肌痉挛性癫痫病相互作用蛋白1抗体
别 名 EPM2A (laforin) interacting protein 1; EPM2A (laforin) IP1; EPM2A-interacting protein 1; EPM2AIP 1; Epm2aip1; EPMIP_HUMAN; FLJ11207; KIAA0766; Laforin interacting protein 1; Laforin-interacting protein; My007.
说 明 书 0.2ml
研究领域 细胞生物 神经生物学 信号转导 转录调节因子
抗体来源 Rabbit
克隆类型 Polyclonal
交叉反应 Human, Mouse, Rat, Dog, Horse,
产品应用 WB=1:100-500 ELISA=1:500-1000 IP=1:20-100 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500 肌痉挛性癫痫病相互作用蛋白1抗体(石蜡切片需做抗原修复)
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 70kDa
性 状 Lyophilized or Liquid
浓 度 1mg/1ml
免 疫 原 KLH conjugated synthetic peptide derived from human EPM2AIP1
亚 型 IgG
纯化方法 affinity purified by Protein A
储 存 液 Preservative: 15mM Sodium Azide, Constituents: 1% BSA, 0.01M PBS, pH 7.4
保存条件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
肌痉挛性癫痫病相互作用蛋白1抗体产品介绍 background:
The EPM2A gene, which encodes laforin, is mutated in an autosomal recessive form of adolescent progressive myoclonus epilepsy. The protein encoded by this gene binds to laforin, but its function is not known. This gene is intronless. [provided by RefSeq, Oct 2008]
Subunit:
Interacts with EPM2A.
Subcellular Location:
Endoplasmic reticulum.
Tissue Specificity:
Expressed in heart, brain, placenta, liver, pancreas, kidney and skeletal muscle.
Gene ID:
9852
Database links:
Entrez Gene: 9852 Human
Entrez Gene: 77781 Mouse
Entrez Gene: 316021 Rat
GenBank: 40353021 Human
Omim: 607911 Human
SwissProt: Q7L775 Human
SwissProt: Q8VEH5 Mouse
Unigene: 28020 Human
Unigene: 209005 Mouse
Unigene: 209819 Rat
Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
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