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上海康朗生物科技有限公司
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Quantity size:

0.2ml

Concentration:

1mg/ml 硫酸软骨素裂解酶抗体  Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

Chondroitinase is a 522 amino acid protein that localizes to the lysosome and functions as an exohydrolase that is essential for the degradation of glycosaminoglycans, keratan sulfate and chondroitin 6-sulfate. Using calcium as a cofactor, Chondroitinase, which 硫酸软骨素裂解酶抗体exists as a disulfide linked oligomer, catalyzes the hydrolysis of the 6-sulfate group on target substrates. Defects in the gene encoding Chondroitinase are the cause of mucopolysaccharidosis type 4A (MPS4A), an autosomal recessive lysosomal storage disease that is characterized by the intracellular accumulation of keratan sulfate and chondroitin-6-sulfate and is associated with dental anomalies, short stature and, in some cases, death in the second or third decade of life.

硫酸软骨素裂解酶抗体Also known as:

Chondroitinase; Chondroitinsulfatase; FLJ00319; FLJ17434; FLJ42844; FLJ98217; Galactosamine (N acetyl) 6 sulfate sulfatase; Galactose 6 sulfate sulfatase; GALNAC6S; GalNAc6S sulfatase; GAS; mFLJ00319; MPS4A; N acetylgalactosamine 6 sulfatase; N acetylgalactosamine 6 sulfate sulfatase; GALNS_HUMAN.

Specificity:

Rabbit Polyclonal IgG, 硫酸软骨素裂解酶抗体affinity purified by Protein A.

Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Horse, Sheep, .

Immunogen: KLH conjugated synthetic peptide derived from human GALNS.

Predicted Molecular Weight: 55kDa.

硫酸软骨素裂解酶抗体Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

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kl405Ra01肌肉磷酸果糖激酶(PFKM)多克隆抗体Polyclonal Antibody to Phosphofructokinase, Muscle (PFKM)

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kl418Ra01肌球蛋白重链7(MYH7)多克隆抗体Polyclonal Antibody to Myosin Heavy Chain 7, Cardiac Muscle, Beta (MYH7)

kl419Ra01肌球蛋白重链6(MYH6)多克隆抗体Polyclonal Antibody to Myosin Heavy Chain 6, Cardiac Muscle, Alpha (MYH6)

kl421Ra01肌球蛋白重链8(MYH8)多克隆抗体Polyclonal Antibody to Myosin Heavy Chain 8, Skeletal Muscle, Perinatal (MYH8)

kl422Hu01肌球蛋白重链9(MYH9)多克隆抗体Polyclonal Antibody to Myosin Heavy Chain 9, Non Muscle (MYH9)

kl423Hu01肌球蛋白重链10(MYH10)多克隆抗体Polyclonal Antibody to Myosin Heavy Chain 10, Non Muscle (MYH10)

kl424Mu01肌球蛋白ⅤA(MYO5A)多克隆抗体Polyclonal Antibody to Myosin VA (MYO5A)

kl440Hu01肌球蛋白ⅦB(MYO7B)多克隆抗体Polyclonal Antibody to Myosin VIIB (MYO7B)

kl449Hu01原肌球蛋白3(TPM3)多克隆抗体Polyclonal Antibody to Tropomyosin 3 (TPM3)

kl452Hu01肌球蛋白轻链9(MYL9)多克隆抗体Polyclonal Antibody to Myosin Light Chain 9, Regulatory (MYL9)

kl466Hu01低氧诱导因子2α(HIF2α)多克隆抗体Polyclonal Antibody to Hypoxia Inducible Factor 2 Alpha (HIF2a)

kl466Mu01低氧诱导因子2α(HIF2α)多克隆抗体Polyclonal Antibody to Hypoxia Inducible Factor 2 Alpha (HIF2a)

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kl493Hu015-羟色胺受体4(HTR4)多克隆抗体Polyclonal Antibody to 5-Hydroxytryptamine Receptor 4 (HTR4)

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