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Quantity size:

0.2ml

Concentration:

1mg/ml 卟胆原脱氨酶抗体  Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

This gene encodes a member of the hydroxymethylbilane synthase superfamily. The encoded protein is the third enzyme of the heme biosynthetic pathway and catalyzes the head to tail condensation of four porphobilinogen molecules into the linear hydroxymethylbilane. Mutations in 卟胆原脱氨酶抗体this gene are associated with the autosomal dominant disease acute intermittent porphyria. Alternatively spliced transcript variants encoding different isoforms have been described. [provided by RefSeq, Jul 2008]

卟胆原脱氨酶抗体Also known as:

HEM3_HUMAN; HMBS; Hydroxymethylbilane synthase; PBG D; PBG-D; PBGD; Porphobilinogen deaminase; Pre uroporphyrinogen synthase; Pre-uroporphyrinogen synthase; UPS; Uroporphyrinogen I synthase; Uroporphyrinogen I synthetase.

Specificity:

Rabbit Polyclonal IgG,卟胆原脱氨酶抗体 affinity purified by Protein A.

Reacts with: Human, Mouse, Rat, Chicken, Pig, Cow, Rabbit, Sheep, Cat, .

Immunogen: KLH conjugated synthetic peptide derived from human HMBS.

Predicted Molecular Weight: 39kDa.

卟胆原脱氨酶抗体Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  IF=1:50-200   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

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kl145Mu01血管内皮生长因子C(VEGFC)多克隆抗体Polyclonal Antibody to Vascular Endothelial Growth Factor C (VEGFC)

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