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上海康朗生物科技有限公司
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Quantity size:

0.2ml

Concentration:

1mg/ml 神经性舞蹈病蛋白抗体  Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

Huntingtin is a protein that contains a polyglutamine region. When the number of glutamine repeats exceeds 35, the gene encodes a version of Huntingtin that leads to Huntington’s disease (HD).神经性舞蹈病蛋白抗体 When the polyglutamine stretch is mutated, Huntingtin acts within the nucleus to induce neurodegeneration by a cell-specific apoptotic mechanism. Loss of Huntingtin activity is unlikely to be the cause of HD, and it has been proposed that the expanded glutamine repeat region may induce an abnormal神经性舞蹈病蛋白抗体 interaction between the mutant protein and other cellular proteins. Huntingtin interacts with a variety of proteins including HAP1, glyceraldehyde phosphate dehydrogenase (GAPDH) and HIP1.

Also known as:

HD; HD protein; HD_HUMAN; HDH; HTT; Huntingtin; HUNTINGTON CHOREA; Huntington disease protein; Huntington's disease protein homolog; IT 15; IT15; OTTMUSP00000026909; 神经性舞蹈病蛋白抗体ZHD; AI256365; C430023I11Rik.

Specificity:

Rabbit Polyclonal IgG, affinity purified by Protein A.

Reacts with: Human, Mouse, Rat, Chicken, Dog, Pig, Cow, Horse, Rabbit, Sheep, .

Immunogen: KLH conjugated synthetic peptide derived from human Huntingt.

神经性舞蹈病蛋白抗体Predicted Molecular Weight: 347kDa.

Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end use

kl383Hu01磷酸肌醇-3-激酶2α肽(PI3K2α)多克隆抗体Polyclonal Antibody to Phosphoinositide-3-Kinase Class-2-Alpha Polypeptide (PIK3C2a)

kl383Mu01磷酸肌醇-3-激酶2α肽(PI3K2α)多克隆抗体Polyclonal Antibody to Phosphoinositide-3-Kinase Class-2-Alpha Polypeptide (PIK3C2a)

kl384Hu01白介素23(IL23)多克隆抗体Polyclonal Antibody to Interleukin 23 (IL23)

kl384Mu01白介素23(IL23)多克隆抗体Polyclonal Antibody to Interleukin 23 (IL23)

kl384Ra01白介素23(IL23)多克隆抗体Polyclonal Antibody to Interleukin 23 (IL23)

kl385Hu01白介素27(IL27)多克隆抗体Polyclonal Antibody to Interleukin 27 (IL27)

kl385Ra01白介素27(IL27)多克隆抗体Polyclonal Antibody to Interleukin 27 (IL27)

kl389Mu01补体成分4a(C4a)多克隆抗体Polyclonal Antibody to Complement Component 4a (C4a)

kl389Ra01补体成分4a(C4a)多克隆抗体Polyclonal Antibody to Complement Component 4a (C4a)

kl391Hu01卵泡抑素(FS)多克隆抗体Polyclonal Antibody to Follistatin (FS)

kl391Mu01卵泡抑素(FS)多克隆抗体Polyclonal Antibody to Follistatin (FS)

kl392Hu01速激肽受体1(TACR1)多克隆抗体Polyclonal Antibody to Tachykinin Receptor 1 (TACR1)

kl394Hu01组织因子通道抑制因子(TFPI)多克隆抗体Polyclonal Antibody to Tissue Factor klhway Inhibitor (TFPI)

kl394Mu01组织因子通道抑制因子(TFPI)多克隆抗体Polyclonal Antibody to Tissue Factor klhway Inhibitor (TFPI)

kl394Ra01组织因子通道抑制因子(TFPI)多克隆抗体Polyclonal Antibody to Tissue Factor klhway Inhibitor (TFPI)

kl394Rb51组织因子通道抑制因子(TFPI)多克隆抗体Polyclonal Antibody to Tissue Factor klhway Inhibitor (TFPI)

kl395Hu01抑制素A(INHA)多克隆抗体Polyclonal Antibody to Inhibin A (INHA)

kl395Po01抑制素A(INHA)多克隆抗体Polyclonal Antibody to Inhibin A (INHA)

kl395Ra01抑制素A(INHA)多克隆抗体Polyclonal Antibody to Inhibin A (INHA)

kl396Hu01性激素结合球蛋白(SHBG)多克隆抗体Polyclonal Antibody to Sex Hormone Binding Globulin (SHBG)

kl396Mu01性激素结合球蛋白(SHBG)多克隆抗体Polyclonal Antibody to Sex Hormone Binding Globulin (SHBG)

kl396Ra01性激素结合球蛋白(SHBG)多克隆抗体Polyclonal Antibody to Sex Hormone Binding Globulin (SHBG)

kl397Hu01转化生长因子β受体Ⅰ(TGFβR1)多克隆抗体Polyclonal Antibody to Transforming Growth Factor Beta Receptor I (TGFbR1)

kl399Ca01高迁移率族蛋白1(HMG1)多克隆抗体Polyclonal Antibody to High Mobility Group Protein 1 (HMG1)

kl399Hu01高迁移率族蛋白1(HMG1)多克隆抗体Polyclonal Antibody to High Mobility Group Protein 1 (HMG1)

kl399Mu01高迁移率族蛋白1(HMG1)多克隆抗体Polyclonal Antibody to High Mobility Group Protein 1 (HMG1)

kl399Po01高迁移率族蛋白1(HMG1)多克隆抗体Polyclonal Antibody to High Mobility Group Protein 1 (HMG1)