资料摘要
资料下载赖氨酸酮戊二酸还原酶抗体 Background: Alpha-aminoadipic semialdehyde synthase (AASS), also designated lysine ketoglutarate reductase (LKR) or saccharopine dehydrogenase (SDH), is a 926 amino acid protein that exists as a homodimer in the mitochondria. AASS acts as a bifunctional enzyme containing the lysine alpha-ketoglutarate reductase (LKR) and saccharopine dehydrogenase activities that catalyzes the first two steps in lysine degradation. It is widely expressed with highest expression in liver and transcription of the AASS gene is induced upon starvation. Mutations in the gene encoding AASS result in various forms familial hyperlysinemias (FH), autosomal recessive disorders characterized by hyperlysinemia, lysinuria, and variable saccharopinuria. However, no adverse mental or physical effects have been found in patients with hyperlysinemia. Also known as: Alpha aminoadipic semialdehyde synthase mitochondrial; LKR/SDH; LKRSDH; LORSDH; Lysine ketoglutarate reductase; Saccharopine dehydrogenase; AASS_HUMAN.赖氨酸酮戊二酸还原酶抗体
文献贡献者
大鼠胰岛素(INS)酶联免疫分析试剂盒
简介：大鼠胰岛素(INS)酶联免疫分析试剂盒用于测定大鼠血清,血浆及相关液体样本中胰岛素(INS)含量。本试剂盒仅供研究使用。
大鼠血管内皮生长因子 (VEGF)酶联免疫分析试剂盒
简介：大鼠血管内皮生长因子 (VEGF)酶联免疫分析试剂盒用于测定大鼠血清，血浆及相关液体样本中血管内皮生长因子 (VEGF)含量。
大鼠胸肾表达趋化因子（BRAK/CXCL14）酶联免疫分析试剂盒
简介：大鼠胸肾表达趋化因子（BRAK/CXCL14）酶联免疫分析试剂盒用于测定大鼠血清、血浆及相关液体样本中胸肾表达趋化因子（BRAK/CXCL14）含量。
大鼠纤维蛋白原(FG)酶联免疫分析试剂盒
简介：大鼠纤维蛋白原(FG)酶联免疫分析试剂盒用于测定大鼠血清血浆及相关液体样本中纤维蛋白原(FG)含量。
大鼠纤溶酶原激活物抑制因子(PAI)酶联免疫分析试剂盒
简介：大鼠纤溶酶原激活物抑制因子(PAI)酶联免疫分析试剂盒用于测定大鼠血清、血浆及相关液体样本中纤溶酶原激活物抑制因子(PAI)含量。
相关产品
关注
拨打电话
留言咨询
