脊髓小脑共济失调2型蛋白抗体

英文名称    ATX2    

中文名称    脊髓小脑共济失调2型蛋白抗体    

别    名    Ataxin 2; ATXN2; Olivopontocerebellar ataxia 2, autosomal dominant; SCA2; Spinocerebellar ataxia type 2 protein; TNRC13; Trinucleotide repeat containing gene 13 protein; SRRT_HUMAN.    

说 明 书    0.2ml      

研究领域    细胞生物  免疫学  神经生物学  表观遗传学      

抗体来源    Rabbit    

克隆类型    Polyclonal    

交叉反应    Human, Mouse, Rat, Chicken, Dog, Pig, Cow, Horse,     

产品应用    WB=1:100-500 ELISA=1:500-1000 IP=1:20-100 IHC-P=1:100-500 IHC-F=1:100-500 IF=1:100-500 脊髓小脑共济失调2型蛋白抗体（石蜡切片需做抗原修复） 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.    

分 子 量    101kDa    

细胞定位    细胞浆     

性    状    Lyophilized or Liquid    

浓    度    1mg/1ml    

免 疫 原    KLH conjugated synthetic peptide derived from human ATX2 (771-815aa)    

亚    型    IgG    

纯化方法    affinity purified by Protein A    

储 存 液    Preservative: 15mM Sodium Azide, Constituents: 1% BSA, 0.01M PBS, pH 7.4    

保存条件    Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C. 

脊髓小脑共济失调2型蛋白抗体产品介绍    background:

The autosomal dominant cerebellar ataxias (ADCA) are a heterogeneous group of neurodegenerative disorders characterized by progressive degeneration of the cerebellum, brain stem and spinal cord. Clinically, ADCA has been divided into three groups: ADCA types I-III. ATX2 belongs to the autosomal dominant cerebellar ataxias type I (ADCA I) which are characterized by cerebellar ataxia in combination with additional clinical features like optic atrophy, ophthalmoplegia, bulbar and extrapyramidal signs, peripheral neuropathy and dementia. ATX2 is caused by expansion of a CAG repeat in the coding region of ATX2. Longer expansions result in earlier onset of the disease. There are four named isoforms.

Subunit:
Monomer. Can also form homodimers.    

脊髓小脑共济失调2型蛋白抗体公司更多热销抗体产品如下：

hz-0297D-hzy5Donkey Anti-human IgG/Cy5  Cy5标记的驴抗人IgG

hz-0297D-hzy5.5Donkey Anti-human IgG/Cy5.5  Cy5.5标记的驴抗人IgG

hz-0297D-hzy7Donkey Anti-human IgG/Cy7  Cy7标记的驴抗人IgG

hz-0297D-PEDonkey Anti-human IgG/PE  PE标记的驴抗人IgG

hz-0297D-PE-hzy3Donkey Anti-human IgG/PE-Cy3  PE-Cy3标记的驴抗人IgG

hz-0297D-PE-hzY5Donkey Anti-human IgG/PE-CY5  PE-CY5标记的驴抗人IgG

hz-0297D-APhzDonkey Anti-human IgG/APC  APC标记的驴抗人IgG

hz-0297D-AF350Donkey Anti-human IgG/Alexa Fluor 350  Alexa Fluor 350标记的驴抗人IgG

hz-0297D-AF488Donkey Anti-human IgG/Alexa Fluor 488  Alexa Fluor 488标记的驴抗人IgG

hz-0297D-AF555Donkey Anti-human IgG/Alexa Fluor 555  Alexa Fluor 555标记的驴抗人IgG

hz-0297D-AF647Donkey Anti-human IgG/Alexa Fluor 647  Alexa Fluor 647标记的驴抗人IgG

hz-0297D-PE-hzy5.5Donkey Anti-human IgG/PE-Cy5.5  PE-Cy5.5标记的驴抗人IgG

hz-0297D-PE-hzy7Donkey Anti-human IgG/PE-Cy7  PE-Cy7标记的驴抗人IgG

hz-0297D-APDonkey Anti-human IgG/AP  碱性磷酸酶（AP）标记的驴抗人IgG

hz-0297D-HRPDonkey Anti-human IgG/HRP  辣根过氧化物酶标记的驴抗人IgG

hz-0297D-BioDonkey Anti-human IgG/Bio  生物素标记的驴抗人IgG

hz-0295D-BioDonkey Anti-rabbit IgG/Bio  生物素标记的驴抗兔IgG

hz-0295D-hzy3Donkey Anti-rabbit IgG/Cy3  Cy3标记的驴抗兔IgG

hz-0295D-hzy5Donkey Anti-rabbit IgG/Cy5  Cy5标记的驴抗兔IgG

hz-0295D-hzy5.5Donkey Anti-rabbit IgG/Cy5.5  Cy5.5标记的驴抗兔IgG

hz-0295D-hzy7Donkey Anti-rabbit IgG/Cy7  Cy7标记的驴抗兔IgG

hz-0295D-PEDonkey Anti-rabbit IgG/PE  PE标记的驴抗兔IgG

hz-0295D-PE-hzy3Donkey Anti-rabbit IgG/PE-Cy3  PE-Cy3标记的驴抗兔IgG

hz-0295D-PE-hzY5Donkey Anti-rabbit IgG/PE-CY5  PE-CY5标记的驴抗兔IgG