腺苷单磷酸脱氨酶1抗体

参考价:¥1
供货周期: 现货
品牌: 康朗生物
规格: 0.1ml/0.2ml
货号: KL2077R
CAS号:
上海康朗生物科技有限公司
银牌会员9年生产商
关注展位 全部试剂
产品详情

?腺苷单磷酸脱氨酶1抗体Quantity size:

0.2ml

Concentration:

1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

AMP deaminase (AMPD) is an allosteric enzyme that plays a critical role in energy metabolism. There are three functional isoforms of AMPD. AMPD1 is the skeletal muscle-specific isoform M located in type II muscle fibers,腺苷单磷酸脱氨酶1抗体 neuromuscular junctions and in capillaries. Defects in AMPD1 are the cause of adenosine monophosphate deaminase deficiency muscle type (AMPDDM). AMPDDM is a metabolic disorder resulting in exercise-related myopathy. It is characterized by exercise-induced muscle aches, cramps, and early fatigue.

腺苷单磷酸脱氨酶1抗体Also known as:

AMPD1; AMPD-1; AMPD1; AMPD-1; Adenosine monophosphate deaminase 1 (isoform M); Adenosine monophosphate deaminase 1; AMP deaminase 1; AMP deaminase isoform M; AMPD 1; Ampd01; MAD; MADA; Myoadenylate deaminase;腺苷单磷酸脱氨酶1抗体 RATAMPD01; AMPD1_MOUSE.

Specificity:

Rabbit Polyclonal IgG, affinity purified by Protein A.

Reacts with: Human, Mouse, Rat, Dog, Cow, Horse, Sheep, .

Immunogen: KLH conjugated synthetic peptide derived from mouse AMP deaminase 1 (125-175aa).

Predicted Molecular Weight: 86kDa.

腺苷单磷酸脱氨酶1抗体Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

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腺苷单磷酸脱氨酶1抗体信息由上海康朗生物科技有限公司为您提供,如您想了解更多关于腺苷单磷酸脱氨酶1抗体报价、型号、参数等信息, 欢迎来电或留言咨询。除供应腺苷单磷酸脱氨酶1抗体外,上海康朗生物科技有限公司还可为您提供腺苷单磷酸活化蛋白激酶β1抗体、磷酸化腺苷单磷酸活化蛋白激酶α1抗体等产品, 公司有专业的客户服务团队,是您值得信赖的合作伙伴。

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