三磷酸腺苷结合盒转运蛋白4抗体

参考价:¥1
供货周期: 现货
品牌: 康朗生物
规格: 0.1ml/0.2ml
货号: KL11908R
CAS号:
上海康朗生物科技有限公司
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三磷酸腺苷结合盒转运蛋白4抗体Quantity size:

0.2ml

Concentration:

1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

The peroxisomal membrane contains several ATP-binding cassette (ABC) transporters, ABCD1-4 that are known to be present in the human peroxisome membrane. All four proteins are ABC half-transporters, which dimerize to form an active transporter. A mutation in the ABCD1 gene causes X-linked adreno-leukodystrophy (X-ALD), a peroxisomal disorder which affects lipid storage. 三磷酸腺苷结合盒转运蛋白4抗体ABCD2 in mouse is expressed at high levels in the brain and adrenal organs, which are adversely affected in X-ALD. The peroxisomal membrane comprises two quantitatively major proteins, PMP22 and ABCD3. ABCD3 is associated with irregularly shaped vesicles which may be defective peroxisomes or peroxisome precursors. ABCD1 localizes to peroxisomes. ABCB7 is a half-transporter involved in the transport of heme from the mitochondria to the cytosol.

三磷酸腺苷结合盒转运蛋白4抗体Also known as:

ABC 41; ABC41; ABCD 4; ABCD4; ABCD4_HUMAN; ATP binding cassette sub family D (ALD) member 4; ATP binding cassette sub family D member 4; ATP-binding cassette sub-family D member 4; P70R antibodyP79R; Peroxisomal membrane protein 1 like; Peroxisomal membrane protein 1-like; Peroxisomal membrane protein 69; PMP 69; PMP69; PMP70-related protein; XMP 1L; PXMP1 L; PXMP1-L; PXMP1L.

三磷酸腺苷结合盒转运蛋白4抗体Specificity:

Rabbit Polyclonal IgG, affinity purified by Protein A.

Reacts with: Human, Mouse, Rat, .

Immunogen: KLH conjugated synthetic peptide derived from human ABCD4.

Predicted Molecular Weight: 69kDa.

三磷酸腺苷结合盒转运蛋白4抗体Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

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三磷酸腺苷结合盒转运蛋白4抗体信息由上海康朗生物科技有限公司为您提供,如您想了解更多关于三磷酸腺苷结合盒转运蛋白4抗体报价、型号、参数等信息, 欢迎来电或留言咨询。除供应三磷酸腺苷结合盒转运蛋白4抗体外,上海康朗生物科技有限公司还可为您提供三磷酸腺柠檬酸裂解酶抗体、三磷酸腺柠檬酸裂解酶抗体等产品, 公司有专业的客户服务团队,是您值得信赖的合作伙伴。

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