遗传性失明相关蛋白AIPL1抗体

?遗传性失明相关蛋白AIPL1抗体Quantity size:

0.2ml

Concentration:

1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

The inherited blindness associated protein, aryl hydrocarbon receptor interacting protein-like 1 (AIPL1), interacts with the cell cycle regulator protein NUB1. AIPL1 is crucial for protein folding and stabilization, as well as for protein trafficking. It localizes to the nucleus or cytoplasm and is highly expressed in the pineal gland and the retina. In the retina,遗传性失明相关蛋白AIPL1抗体AIPL1 is expressed in both developing cone and rod photoreceptors, but it is restricted to rod photoreceptors in the adult human retina. Defects in the gene encoding for AIPL1 can cause Leber congenital amaurosis type IV, an early-onset, inherited autosomal recessive disorder that results in childhood blindness.

遗传性失明相关蛋白AIPL1抗体Also known as:

A930007I01Rik; Aipl1; AIPL1_HUMAN; AIPL2; Aryl hydrocarbon interacting protein like 1; Aryl hydrocarbon receptor interacting protein like 1; Aryl-hydrocarbon-interacting protein-like 1; LCA4; MGC25485;遗传性失明相关蛋白AIPL1抗体 OTTHUMP00000128207; OTTMUSP00000006382; RP23-401C17.1.

Specificity:

●

Rabbit Polyclonal IgG, affinity purified by Protein A.

●

Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Rabbit, Sheep, .

●

Immunogen: KLH conjugated synthetic peptide derived from human AIPL1.

●

Predicted Molecular Weight: 44kDa.

遗传性失明相关蛋白AIPL1抗体Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

kl239Hu01甲状腺素受体α(THRα)多克隆抗体Polyclonal Antibody to Thyroid Hormone Receptor Alpha (THRa)

kl239Ra01甲状腺素受体α(THRα)多克隆抗体Polyclonal Antibody to Thyroid Hormone Receptor Alpha (THRa)

kl241Hu01端粒酶逆转录酶(TERT)多克隆抗体Polyclonal Antibody to Telomerase Reverse Transcriptase (TERT)

kl242Hu01核仁素(NCL)多克隆抗体Polyclonal Antibody to Nucleolin (NCL)

kl242Mu01核仁素(NCL)多克隆抗体Polyclonal Antibody to Nucleolin (NCL)

kl243Hu01拓扑异构酶Ⅰ(TOP1)多克隆抗体Polyclonal Antibody to Topoisomerase I (TOP1)

kl246Mu01磷酸肌醇依赖性蛋白激酶1(PDPK1)多克隆抗体Polyclonal Antibody to Phosphoinositide Dependent Protein Kinase 1 (PDPK1)

kl257Hu0162kDa核孔蛋白(NUP62)多克隆抗体Polyclonal Antibody to Nucleoporin 62kDa (NUP62)

kl260Hu01融合蛋白(FUS)多克隆抗体Polyclonal Antibody to Fusion (FUS)

kl260Mu01融合蛋白(FUS)多克隆抗体Polyclonal Antibody to Fusion (FUS)

kl262Hu01紧密连接蛋白1(TJP1)多克隆抗体Polyclonal Antibody to Tight Junction Protein 1 (TJP1)

kl268Hu0111-β-羟基类固醇脱氢酶1(HSD11β1)多克隆抗体Polyclonal Antibody to 11-Beta-Hydroxysteroid Dehydrogenase Type 1 (HSD11b1)

kl268Ra0111-β-羟基类固醇脱氢酶1(HSD11β1)多克隆抗体Polyclonal Antibody to 11-Beta-Hydroxysteroid Dehydrogenase Type 1 (HSD11b1)

kl270Hu017-脱氢胆固醇还原酶(DHCR7)多克隆抗体Polyclonal Antibody to 7-Dehydrocholesterol Reductase (DHCR7)

kl276Hu01氨基酰化酶1(ACY1)多克隆抗体Polyclonal Antibody to Aminoacylase 1 (ACY1)