供货周期: | 现货 |
品牌: | 康朗生物 |
规格: | 0.1ml/0.2ml |
货号: | KL17208R |
CAS号: |
脊髓小脑性共济失调蛋白3抗体Quantity size:
0.2ml
Concentration:
1mg/ml Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Machado-Joseph disease, also known as spinocerebellar ataxia-3, is an autosomal dominant neurologic disorder. The protein encoded by this gene contains (CAG)n repeats in the coding region,脊髓小脑性共济失调蛋白3抗体 and the expansion of these repeats from the normal 13-36 to 68-79 is one cause of Machado-Joseph disease. There is a negative correlation between the age of onset and CAG repeat numbers. Alternatively spliced transcript variants encoding different isoforms have been described for this gene. [provided by RefSeq, Sep 2009]
脊髓小脑性共济失调蛋白3抗体Also known as:
AT3; Ataxin 3; Ataxin-3; ATX3; ATX3_HUMAN; ATXN3; EC 3.4.22.; JOS; Josephin; Machado Joseph disease (spinocerebellar ataxia 3, olivopontocerebellar ataxia 3, autosomal dominant, ataxin 3); Machado Joseph disease; Machado Joseph disease protein 1; Machado-Joseph disease protein 1; Machado-Joseph disease protein 1 homolog; MJD; MJD gene; MJD1; Olivopontocerebellar ataxia 3; OTTHUMP00000221583; OTTHUMP00000221585; OTTHUMP00000221586;脊髓小脑性共济失调蛋白3抗体 OTTHUMP00000221587; OTTHUMP00000231995; OTTHUMP00000231997; Rsca3; SCA3; SCA3 gene; Spinocerebellar ataxia type 3 protein.
Specificity:
●
Rabbit Polyclonal IgG, affinity purified by Protein A.
●
Reacts with: Human, Mouse, Rat, .
●
Immunogen: KLH conjugated synthetic peptide derived from human Ataxin 3.
●
脊髓小脑性共济失调蛋白3抗体Predicted Molecular Weight: 42kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user
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kl101Mu01基质金属蛋白酶3(MMP3)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 3 (MMP3)
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kl101Ra01基质金属蛋白酶3(MMP3)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 3 (MMP3)
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kl102Eq01基质金属蛋白酶7(MMP7)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 7 (MMP7)
kl102Hu01基质金属蛋白酶7(MMP7)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 7 (MMP7)
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kl102Ra01基质金属蛋白酶7(MMP7)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 7 (MMP7)
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kl104Gu01胆囊收缩素A受体(CCKAR)多克隆抗体Polyclonal Antibody to Cholecystokinin A Receptor (CCKAR)
kl104Hu01胆囊收缩素A受体(CCKAR)多克隆抗体Polyclonal Antibody to Cholecystokinin A Receptor (CCKAR)
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