供货周期: | 现货 |
品牌: | 康朗生物 |
型号: | 0.1ml/0.2ml |
货号: | KL18333R |
Quantity size:
0.2ml
Concentration:
1mg/ml 卷曲螺旋结构域蛋白126抗体 Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
CCDC126 is a 140 amino acid secreted protein encoded by a gene mapping to human chromosome 7. Chromosome 7 is about 158 milllion bases long, encodes over 1000 genes and makes up about 5% of the human genome. Chromosome 7 has been linked to Osteogenesis imperfecta, Pendred syndrome,卷曲螺旋结构域蛋白126抗体 Lissencephaly, Citrullinemia and Shwachman-Diamond syndrome. The deletion of a portion of the q arm of chromosome 7 is associated with Williams-Beuren syndrome, a condition characterized by mild mental retardation, an unusual comfort and friendliness with strangers and an elfin appearance. Deletions of portions of the q arm of chromosome 7 are also seen in a number of myeloid disorders including cases of acute myelogenous leukemia and myelodysplasia.
卷曲螺旋结构域蛋白126抗体Also known as:
LOC90693; alpha 1,3(6) mannosylglycoprotein; beta 1,6 N acetyl glucosaminyltransferase like; CC126_HUMAN; Ccdc126; coiled coil domain containing 126; Coiled-coil domain-containing protein 126; FLJ23031; MGC104248; OTTHUMP00000158577.
Specificity:
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Rabbit Polyclonal IgG, 卷曲螺旋结构域蛋白126抗体affinity purified by Protein A.
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Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Horse, Rabbit, Sheep, .
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Immunogen: KLH conjugated synthetic peptide derived from human CCDC126.
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Predicted Molecular Weight: 13kDa.
Storage:
卷曲螺旋结构域蛋白126抗体Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
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