膜蛋白EVC2抗体

参考价:面议
供货周期: 现货
品牌: 康朗生物
规格: 0.1ml/0.2ml
货号: KL6638R
CAS号:
上海康朗生物科技有限公司
银牌会员9年生产商
关注展位 全部试剂
产品详情

Quantity size:

0.2ml

Concentration:

1mg/ml 膜蛋白EVC2抗体  Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

EVC2 is an integral membrane protein that plays a vital role in bone formation and skeletal development. Defects in EVC2 are a cause of Ellis-van Creveld syndrome (EVC), also known as chondroectodermal dysplasia.膜蛋白EVC2抗体 EVC is an autosomal recessive disorder characterized by the clinical tetrad of chondrodystrophy, polydactyly, ectodermal dysplasia and cardiac anomalies. Patients manifest short-limb 膜蛋白EVC2抗体dwarfism, short ribs, postaxial polydactyly and dysplastic nails and teeth. Congenital heart defects, most commonly an atrioventricular septal defect, are observed in 60% of affected individuals.

Also known as:

膜蛋白EVC2抗体Ellis van Creveld syndrome 2; LBN; Limbin; LBN_HUMAN.

Specificity:

Rabbit Polyclonal IgG, affinity purified by Protein A.

Reacts with: Human, .

Immunogen: KLH conjugated synthetic peptide derived from human EVC2 (11.

Predicted Molecular Weight: 145kDa.

膜蛋白EVC2抗体Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

kl876Mu01Sestrin 3蛋白(SESN3)多克隆抗体Polyclonal Antibody to Sestrin 3 (SESN3)

kl877Mu01Sestrin 1蛋白(SESN1)多克隆抗体Polyclonal Antibody to Sestrin 1 (SESN1)

kl878Hu01分泌型卷曲相关蛋白4(SFRP4)多克隆抗体Polyclonal Antibody to Secreted Frizzled Related Protein 4 (SFRP4)

kl878Mu01分泌型卷曲相关蛋白4(SFRP4)多克隆抗体Polyclonal Antibody to Secreted Frizzled Related Protein 4 (SFRP4)

kl879Hu01分泌型卷曲相关蛋白2(SFRP2)多克隆抗体Polyclonal Antibody to Secreted Frizzled Related Protein 2 (SFRP2)

kl880Hu01分泌型卷曲相关蛋白1(SFRP1)多克隆抗体Polyclonal Antibody to Secreted Frizzled Related Protein 1 (SFRP1)

kl880Mu01分泌型卷曲相关蛋白1(SFRP1)多克隆抗体Polyclonal Antibody to Secreted Frizzled Related Protein 1 (SFRP1)

kl880Ra01分泌型卷曲相关蛋白1(SFRP1)多克隆抗体Polyclonal Antibody to Secreted Frizzled Related Protein 1 (SFRP1)

kl891Hu01中间丝蛋白(SYNC)多克隆抗体Polyclonal Antibody to Syncoilin (SYNC)

kl897Hu01钙调蛋白样蛋白5(CALML5)多克隆抗体Polyclonal Antibody to Calmodulin Like Protein 5 (CALML5)

kl898Hu01钙调蛋白样蛋白3(CALML3)多克隆抗体Polyclonal Antibody to Calmodulin Like Protein 3 (CALML3)

kl900Hu01含硬化蛋白域蛋白1(SOSTDC1)多克隆抗体Polyclonal Antibody to Sclerostin Domain Containing Protein 1 (SOSTDC1)

kl913Hu01斯钙素2(STC2)多克隆抗体Polyclonal Antibody to Stanniocalcin 2 (STC2)

kl914Hu01核苷酸还原酶M1(RRM1)多克隆抗体Polyclonal Antibody to Ribonucleotide Reductase M1 (RRM1)

kl952Hu01核膜含血影蛋白重复蛋白2(Nesp2)多克隆抗体Polyclonal Antibody to Nesprin 2 (Nesp2)

kl953Hu01核膜含血影蛋白重复蛋白1(Nesp1)多克隆抗体Polyclonal Antibody to Nesprin 1 (Nesp1)

kl975Hu01双特异性磷酸酶5(DUSP5)多克隆抗体Polyclonal Antibody to Dual Specificity Phosphatase 5 (DUSP5)

kl975Mu01双特异性磷酸酶5(DUSP5)多克隆抗体Polyclonal Antibody to Dual Specificity Phosphatase 5 (DUSP5)


膜蛋白EVC2抗体信息由上海康朗生物科技有限公司为您提供,如您想了解更多关于膜蛋白EVC2抗体报价、型号、参数等信息, 欢迎来电或留言咨询。除供应膜蛋白EVC2抗体外,上海康朗生物科技有限公司还可为您提供人棕榈酰化膜蛋白6检测试剂盒、人棕榈酰化膜蛋白2检测试剂盒等产品, 公司有专业的客户服务团队,是您值得信赖的合作伙伴。

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