肌萎缩侧索硬化症相关蛋白FGGY抗体

参考价:面议
供货周期: 现货
品牌: 康朗生物
规格: 0.1ml/0.2ml
货号: KL11689R
CAS号:
上海康朗生物科技有限公司
银牌会员9年生产商
关注展位 全部试剂
产品详情

Quantity size:

0.2ml

Concentration:

1mg/ml 肌萎缩侧索硬化症相关蛋白FGGY抗体  Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

FGGY is a 551 amino acid member of the FGGY kinase family that exists as four isoforms which are produced by alternative splicing events. Expressed in lung, kidney, small intestine, liver and fetal brain, FGGY is encoded by a gene that maps to chromosome 1 and, when mutated, 肌萎缩侧索硬化症相关蛋白FGGY抗体is associated with sporadic amyotrophic lateral sclerosis (ALS). ALS is a neurodegenerative disorder that affects motor neurons and results in fatal paralysis, usually within 2 to 5 years after initial diagnosis. Chromosome 1, on which the gene encoding FGGY is located, is the largest human chromosome, spanning about 260 million base pairs and making up 8% of the human genome.肌萎缩侧索硬化症相关蛋白FGGY抗体 There are about 3,000 genes on chromosome 1, many of which are associated with genetic diseases, including Hutchinson-Gilford progeria, familial adenomatous polyposis, Stickler syndrome, Gaucher disease and Usher syndrome.

肌萎缩侧索硬化症相关蛋白FGGY抗体Also known as:

fggy; FGGY carbohydrate kinase domain containing; FGGY carbohydrate kinase domain-containing protein; FGGY_HUMAN; FLJ10986; MGC94804; OTTHUMP00000010078; OTTHUMP00000010081; OTTHUMP00000010082; OTTHUMP00000202071; RP11-242B9.1.

Specificity:

Rabbit Polyclonal IgG, affinity purified by Protein A.

Reacts with: Human, Mouse, Rat, Dog, Cow, Horse, Rabbit, Sheep, .

Immunogen: KLH conjugated synthetic peptide derived from human FGGY (15.

Predicted Molecular Weight: 60kDa.

肌萎缩侧索硬化症相关蛋白FGGY抗体Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

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肌萎缩侧索硬化症相关蛋白FGGY抗体信息由上海康朗生物科技有限公司为您提供,如您想了解更多关于肌萎缩侧索硬化症相关蛋白FGGY抗体报价、型号、参数等信息, 欢迎来电或留言咨询。除供应肌萎缩侧索硬化症相关蛋白FGGY抗体外,上海康朗生物科技有限公司还可为您提供人纤维蛋白原γ检测试剂盒、FGγ检测试剂盒等产品, 公司有专业的客户服务团队,是您值得信赖的合作伙伴。

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