α-半乳糖苷酶抗体

Quantity size:

0.2ml

Concentration:

1mg/ml  α-半乳糖苷酶抗体 Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

Galactosidase alpha is involved in the hydrolysis of terminal, non reducing alpha D galactose residues in alpha D galactosides, including galactose oligosaccharides, galactomannans and galactohydrolase. Defects in GLA are the cause of Fabry's disease (FD). FD is a rare α-半乳糖苷酶抗体X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. Clinical recognition in males results from characteristic skin lesions (angiokeratomas) over the lower trunk. Patients may show ocular deposits, febrile episodes, and burning pain in the extremities. Death results from α-半乳糖苷酶抗体renal failure, cardiac or cerebral complications of hypertension or other vascular disease. Heterozygous females may exhibit the disorder in an attenuated form, they are more likely to show corneal opacities.

Also known as:

Galactosidase alpha; Alpha D galactosidase A; Alpha D galactoside galactohydrolase; Melibiase; Alpha galactosidase A; GALA; GLA; GLA protein; AGAL_HUMAN.

Specificity:

●

Rabbit Polyclonal IgG, α-半乳糖苷酶抗体affinity purified by Protein A.

●

Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Rabbit, .

●

Immunogen: KLH conjugated synthetic peptide derived from human Galactos.

●

Predicted Molecular Weight: 45kDa.

α-半乳糖苷酶抗体Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

kl427Ra01Ras相关C3肉毒菌毒素底物1(Rac1)多克隆抗体Polyclonal Antibody to Ras Related C3 Botulinum Toxin Substrate 1 (Rac1)

kl435Hu01甘油磷酸肌醇锚定高密度脂蛋白结合蛋白1(GPIHBP1)多克隆抗体Polyclonal Antibody to Glycosylphosphatidylinositol Anchored High Density Lipoprotein Binding Protein 1 (GPIHBP1)

kl464Hu01饥饿素-O-乙酰基转移酶(GOAT)多克隆抗体Polyclonal Antibody to Ghrelin-O-Acyltransferase (GOAT)

kl546Mu01Lin-28同源物A(LIN28A)多克隆抗体Polyclonal Antibody to Lin-28 Homolog A (LIN28A)

kl563Hu01ⅣD组磷脂酶A2(PLA2G4D)多克隆抗体Polyclonal Antibody to Phospholikle A2, Group IVD (PLA2G4D)

kl611Hu01POTE锚蛋白域家族成员G(POTEG)多克隆抗体Polyclonal Antibody to POTE Ankyrin Domain Family, Member G (POTEG)

kl635Hu01牙骨质蛋白1(CEMP1)多克隆抗体Polyclonal Antibody to Cementum Protein 1 (CEMP1)

kl658Hu01防御素β103B(DEFβ103B)多克隆抗体Polyclonal Antibody to Defensin Beta 103B (DEFB103B)

kl667Hu01结肠癌转移关联基因1(MACC1)多克隆抗体Polyclonal Antibody to Metastasis Associated In Colon Cancer 1 (MACC1)

kl679Hu01RAS癌基因家族成员RAB37(RAB37)多克隆抗体Polyclonal Antibody to RAB37, Member RAS Oncogene Family (RAB37)

kl762Hu01干扰素诱导内质网关联病毒抑制蛋白(Viperin)多克隆抗体Polyclonal Antibody to Virus Inhibitory Protein (Viperin)

kl767Hu01锌指同源框蛋白4(ZFHX4)多克隆抗体Polyclonal Antibody to Zinc Finger Homeobox Protein 4 (ZFHX4)

kl802Hu01结侧蛋白(JN)多克隆抗体Polyclonal Antibody to Juxtanodin (JN)

kl893Hu01含RNA结合冷休克域蛋白E1(CSDE1)多克隆抗体Polyclonal Antibody to Cold Shock Domain Containing Protein E1, RNA Binding (CSDE1)

kl021Hu01RNA结合基元蛋白20(RBM20)多克隆抗体Polyclonal Antibody to RNA Binding Motif Protein 20 (RBM20)

kl048Hu01HtrA丝氨酸肽酶4(HTRA4)多克隆抗体Polyclonal Antibody to HtrA Serine Peptidase 4 (HTRA4)

kl221Hu01Dermokine蛋白(DMKN)多克隆抗体Polyclonal Antibody to Dermokine (DMKN)

kl237Hu01肝细胞癌相关蛋白1(HCRP1)多克隆抗体Polyclonal Antibody to Heklocellular Carcinoma Related Protein 1 (HCRP1)

kl251Hu01Adropin蛋白(AD)多克隆抗体Polyclonal Antibody to Adropin (AD)

kl280Hu01食道癌相关基因4(ECRG4)多克隆抗体Polyclonal Antibody to Esophageal Cancer Related Gene 4 (ECRG4)

kl341Hu01CD200受体1(CD200R1)多克隆抗体Polyclonal Antibody to CD200 Receptor 1 (CD200R1)

kl468Hu01血管生成素样蛋白6(ANGPTL6)多克隆抗体Polyclonal Antibody to Angiopoietin Like Protein 6 (ANGPTL6)

kl468Ra01血管生成素样蛋白6(ANGPTL6)多克隆抗体Polyclonal Antibody to Angiopoietin Like Protein 6 (ANGPTL6