β-葡萄糖脑苷脂酶抗体

Quantity size:

0.2ml

Concentration:

1mg/ml β-葡萄糖脑苷脂酶抗体  Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

This gene encodes a lysosomal membrane protein that cleaves the beta-glucosidic linkage of glycosylceramide, an intermediate in glycolipid metabolism. Mutations in this gene cause Gaucher disease, a lysosomal storage disease characterized by an accumulation of glucocerebrosidesβ-葡萄糖脑苷脂酶抗体. A related pseudogene is approximately 12 kb downstream of this gene on chromosome 1. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jan 2010]

β-葡萄糖脑苷脂酶抗体Also known as:

Glucosidase beta; Acid beta glucosidase; Acid beta-glucosidase; Alglucerase; Beta glucocerebrosidase; BETA GLUCOSIDASE, ACID; Beta-glucocerebrosidase; betaGC; D glucosyl N acylsphingosine glucohydrolase; D-glucosyl-N-acylsphingosine glucohydrolase; EC 3.2.1.45 ; GBA; Gba protein; GBA1; GC antibody GCase; GCB; GLCM_HUMAN; GLUC; Glucocerebrosidase (alt.); Glucocerebrosidase; GLUCOCEREBROSIDASE PSEUDOGENE; Glucosidase beta; β-葡萄糖脑苷脂酶抗体Glucosidase, beta, acid; Glucosidase, beta; acid (includes glucosylceramidase); Glucosylceramidase; Imiglucerase; Lysosomal glucocerebrosidase.

Specificity:

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Rabbit Polyclonal IgG, affinity purified by Protein A.

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Reacts with: Human, Mouse, Rat, Rabbit, .

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Immunogen: KLH conjugated synthetic peptide derived from human Glucosid.

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β-葡萄糖脑苷脂酶抗体Predicted Molecular Weight: 56kDa.

Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

kl473Hu01C组着色性干皮病偶联因子(XPC)多克隆抗体Polyclonal Antibody to Xeroderma Pigmentosum, Complementation Group C (XPC)

kl473Mu01C组着色性干皮病偶联因子(XPC)多克隆抗体Polyclonal Antibody to Xeroderma Pigmentosum, Complementation Group C (XPC)

kl474Hu01甲状旁腺素受体2(PTHR2)多克隆抗体Polyclonal Antibody to klathyroid Hormone Receptor 2 (PTHR2)

kl474Ra01甲状旁腺素受体2(PTHR2)多克隆抗体Polyclonal Antibody to klathyroid Hormone Receptor 2 (PTHR2)

kl475Hu01维生素D受体(VDR)多克隆抗体Polyclonal Antibody to Vitamin D Receptor (VDR)

kl475Mu01维生素D受体(VDR)多克隆抗体Polyclonal Antibody to Vitamin D Receptor (VDR)

kl476Hu01半胱氨酸蛋白酶抑制剂A(CSTA)多克隆抗体Polyclonal Antibody to Cystatin A (CSTA)

kl478Hu01心肌肌钙蛋白I(TNNI3)多克隆抗体Polyclonal Antibody to Troponin I Type 3, Cardiac (TNNI3)

kl478Mu01心肌肌钙蛋白I(TNNI3)多克隆抗体Polyclonal Antibody to Troponin I Type 3, Cardiac (TNNI3)

kl478Po01心肌肌钙蛋白I(TNNI3)多克隆抗体Polyclonal Antibody to Troponin I Type 3, Cardiac (TNNI3)

kl478Ra01心肌肌钙蛋白I(TNNI3)多克隆抗体Polyclonal Antibody to Troponin I Type 3, Cardiac (TNNI3)

kl480Po01肌红蛋白(MYO)多克隆抗体Polyclonal Antibody to Myoglobin (MYO)

kl483Hu01内皮素转化酶1(ECE1)多克隆抗体Polyclonal Antibody to Endothelin Converting Enzyme 1 (ECE1)

kl483Mu01内皮素转化酶1(ECE1)多克隆抗体Polyclonal Antibody to Endothelin Converting Enzyme 1 (ECE1)

kl484Hu01氨基端前心钠肽(NT-ProANP)多克隆抗体Polyclonal Antibody to N-Terminal Pro-Atrial Natriuretic Peptide (NT-ProANP)

kl484Mu01氨基端前心钠肽(NT-ProANP)多克隆抗体Polyclonal Antibody to N-Terminal Pro-Atrial Natriuretic Peptide (NT-ProANP)

kl484Ra01氨基端前心钠肽(NT-ProANP)多克隆抗体Polyclonal Antibody to N-Terminal Pro-Atrial Natriuretic Peptide (NT-ProANP)

kl488Hu01角蛋白5(KRT5)多克隆抗体Polyclonal Antibody to Keratin 5 (KRT5)

kl489Hu01角蛋白4(KRT4)多克隆抗体Polyclonal Antibody to Keratin 4 (KRT4)