半乳糖瓦尔登转化酶抗体

参考价:面议
供货周期: 现货
品牌: 康朗生物
规格: 0.1ml/0.2ml
货号: KL13265R
CAS号:
上海康朗生物科技有限公司
银牌会员9年生产商
关注展位 全部试剂
产品详情

Quantity size:

0.2ml

Concentration:

1mg/ml 半乳糖瓦尔登转化酶抗体  Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

This gene encodes UDP-galactose-4-epimerase which catalyzes two distinct but analogous reactions: the epimerization of UDP-glucose to UDP-galactose, and the epimerization of UDP-N-acetylglucosamine to UDP-N-acetylgalactosamine. The bifunctional nature of the enzyme has the important metabolic consequence that mutant cells (or individuals) are半乳糖瓦尔登转化酶抗体 dependent not only on exogenous galactose, but also on exogenous N-acetylgalactosamine as a necessary precursor for the synthesis of glycoproteins and glycolipids. Mutations in this gene result in epimerase-deficiency galactosemia, also referred to as galactosemia type 3, a 半乳糖瓦尔登转化酶抗体disease characterized by liver damage, early-onset cataracts, deafness and mental retardation, with symptoms ranging from mild ('peripheral' form) to severe ('generalized' form). Multiple alternatively spliced transcripts encoding the same protein have been identified. [provided by RefSeq, Jul 2008]

Also known as:

FLJ95174; FLJ97302; Galactose 4 epimerase UDP; Galactowaldenase; galE; GALE_HUMAN; OTTHUMP00000002991; OTTHUMP00000002994; OTTHUMP00000037931; OTTHUMP00000044857; SDR1E1; short chain dehydrogenase/reductase family 1E member 1; UDP galactose 4 epimerase; UDP glucose 4 epimerase;半乳糖瓦尔登转化酶抗体 UDP-galactose 4-epimerase; UDP-glucose 4-epimerase.

Specificity:

Rabbit Polyclonal IgG, affinity purified by Protein A.

Reacts with: Human, Mouse, Rat, Pig, Horse, .

Immunogen: KLH conjugated synthetic peptide derived from human GALE/Gal.

半乳糖瓦尔登转化酶抗体Predicted Molecular Weight: 38kDa.

Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

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kl152Mu01衰老关键蛋白2(FBLN2)多克隆抗体Polyclonal Antibody to Fibulin 2 (FBLN2)

kl158Hu01S100钙结合蛋白A14(S100A14)多克隆抗体Polyclonal Antibody to S100 Calcium Binding Protein A14 (S100A14)

kl161Hu01N-乙酰α-D-氨基葡萄糖苷酶(NAGLU)多克隆抗体Polyclonal Antibody to N-Acetyl Alpha-D-Glucosaminidase (NAGLU)

kl163Hu01核糖核酸酶Ⅲ(RNASEN)多克隆抗体Polyclonal Antibody to Ribonuclease III, Nuclear (RNASEN)

kl164Hu01核糖核酸酶L(RNASEL)多克隆抗体Polyclonal Antibody to Ribonuclease L (RNASEL)

kl171Hu01同线蛋白2(ST2)多克隆抗体Polyclonal Antibody to Syntenin 2 (ST2)

kl172Hu01多配体蛋白聚糖3(SDC3)多克隆抗体Polyclonal Antibody to Syndecan 3 (SDC3)

kl177Hu01对氧磷酶2(PON2)多克隆抗体Polyclonal Antibody to klaoxonase 2 (PON2)

kl178Hu01对氧磷酶3(PON3)多克隆抗体Polyclonal Antibody to klaoxonase 3 (PON3)

kl180Hu01核连蛋白2(NUCB2)多克隆抗体Polyclonal Antibody to Nucleobindin 2 (NUCB2)

kl186Hu01蔗糖酶异麦芽糖酶(SI)多克隆抗体Polyclonal Antibody to Sucrase Isomaltase (SI)

kl190Hu01核糖核酸酶A4(RNASE4)多克隆抗体Polyclonal Antibody to Ribonuclease A4 (RNASE4)

kl191Hu01核糖核酸酶A8(RNASE8)多克隆抗体Polyclonal Antibody to Ribonuclease A8 (RNASE8)

kl192Hu01核糖核酸酶A6(RNASE6)多克隆抗体Polyclonal Antibody to Ribonuclease A6 (RNASE6)

kl193Hu01核糖核酸酶A7(RNASE7)多克隆抗体Polyclonal Antibody to Ribonuclease A7 (RNASE7)

kl194Hu01Ⅱ型胶原α1(COL2α1)多克隆抗体Polyclonal Antibody to Collagen Type II Alpha 1 (COL2a1)

kl194Ra01Ⅱ型胶原α1(COL2α1)多克隆抗体Polyclonal Antibody to Collagen Type II Alpha 1 (COL2a1)

kl195Hu01Ⅲ型胶原α1(COL3α1)多克隆抗体Polyclonal Antibody to Collagen Type III Alpha 1 (COL3a1)

kl195Ra01Ⅲ型胶原α1(COL3α1)多克隆抗体Polyclonal Antibody to Collagen Type III Alpha 1 (COL3a1)

kl196Hu01转运蛋白2(TNPO2)多克隆抗体Polyclonal Antibody to Transportin 2 (TNPO2)

kl198Hu01死骨片1(SQSTM1)多克隆抗体Polyclonal Antibody to Sequestosome 1 (SQSTM1)

kl202Mu01染色质域解旋酶DNA结合蛋白4(CHD4)多克隆抗体Polyclonal Antibody to Chromodomain Helicase DNA Binding Protein 4 (CHD4)

kl206Mu01EB病毒诱导蛋白3(EBI3)多克隆抗体Polyclonal Antibody to Epstein Barr Virus Induced Protein 3 (EBI3)


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