溶酶体累积病相关蛋白/口吃相关蛋白抗体

参考价:面议
供货周期: 现货
品牌: 康朗生物
规格: 0.1ml/0.2ml
货号: KL13476R
CAS号:
上海康朗生物科技有限公司
银牌会员9年生产商
关注展位 全部试剂
产品详情

Quantity size:

0.2ml

Concentration:

1mg/ml 溶酶体累积病相关蛋白/口吃相关蛋白抗体  Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

This gene encodes two of three subunit types of the membrane-bound enzyme N-acetylglucosamine-1-phosphotransferase, a heterohexameric complex composed of two alpha, two beta, and two gamma subunits. The encoded protein is proteolytically cleaved at the Lys928-Asp929 bond to yield mature alpha and beta polypeptides while the gamma subunits are the product 溶酶体累积病相关蛋白/口吃相关蛋白抗体of a distinct gene (GeneID 84572). In the Golgi apparatus, the heterohexameric complex catalyzes the first step in the synthesis of mannose 6-phosphate recognition markers on certain oligosaccharides of newly synthesized lysosomal enzymes. These recognition markers are essential for appropriate trafficking of lysosomal enzymes. Mutations in this gene have been associated with both mucolipidosis II and mucolipidosis IIIA.[provided by RefSeq, May 2010].

溶酶体累积病相关蛋白/口吃相关蛋白抗体Also known as:

N-acetylglucosamine-1-phosphotransferase subunit beta; EC=2.7.8.17; GlcNAc-1-phosphotransferase subunits alpha/beta; GNPTA; GNPTA_HUMAN; Gnptab; KIAA1208; Stealth protein GNPTAB; UDP-N-acetylglucosamine-1-phosphotransferase subunits alpha/beta.

Specificity:

Rabbit Polyclonal IgG,溶酶体累积病相关蛋白/口吃相关蛋白抗体 affinity purified by Protein A.

Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Sheep, .

Immunogen: KLH conjugated synthetic peptide derived from human N-acetyl.

Predicted Molecular Weight: 39kDa.

溶酶体累积病相关蛋白/口吃相关蛋白抗体Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

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kl744Hu01泛素D(UBD)多克隆抗体Polyclonal Antibody to Ubiquitin D (UBD)

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kl750Hu01肿瘤坏死因子配体超家族成员13(TNFSF13)多克隆抗体Polyclonal Antibody to Tumor Necrosis Factor Ligand Superfamily, Member 13 (TNFSF13)

kl750Mu01肿瘤坏死因子配体超家族成员13(TNFSF13)多克隆抗体Polyclonal Antibody to Tumor Necrosis Factor Ligand Superfamily, Member 13 (TNFSF13)

kl752Hu01Ⅰ类主要组织相容性复合体E(MHCE)多克隆抗体Polyclonal Antibody to Major Histocomklibility Complex Class I E (MHCE)

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kl758Hu01核糖核酸酶A3(RNASE3)多克隆抗体Polyclonal Antibody to Ribonuclease A3 (RNASE3)

kl759Hu01羟甲基戊二酰辅酶A合酶(HMGCS)多克隆抗体Polyclonal Antibody to Hydroxymethylglutaryl Coenzyme A Synthase (HMGCS)

kl760Hu01再生胰岛衍生蛋白1α(REG1α)多克隆抗体Polyclonal Antibody to Regenerating Islet Derived Protein 1 Alpha (REG1a)

kl760Ra01再生胰岛衍生蛋白1α(REG1α)多克隆抗体Polyclonal Antibody to Regenerating Islet Derived Protein 1 Alpha (REG1a)

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kl766Mu01可溶性半乳糖凝集素3结合蛋白(LGALS3BP)多克隆抗体Polyclonal Antibody to Lectin Galactoside Binding, Soluble 3 Binding Protein (LGALS3BP)

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kl769Hu01S100钙结合蛋白A6(S100A6)多克隆抗体Polyclonal Antibody to S100 Calcium Binding Protein A6 (S100A6)


溶酶体累积病相关蛋白/口吃相关蛋白抗体信息由上海康朗生物科技有限公司为您提供,如您想了解更多关于溶酶体累积病相关蛋白/口吃相关蛋白抗体报价、型号、参数等信息, 欢迎来电或留言咨询。除供应溶酶体累积病相关蛋白/口吃相关蛋白抗体外,上海康朗生物科技有限公司还可为您提供人溶酶体酸性磷酸酶2检测试剂盒、人溶酶体关联膜蛋白2检测试剂盒等产品, 公司有专业的客户服务团队,是您值得信赖的合作伙伴。

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