三羟基三甲基辅酶A裂解酶抗体

参考价:面议
供货周期: 现货
品牌: 康朗生物
规格: 0.1ml/0.2ml
货号: KL5067R
CAS号:
上海康朗生物科技有限公司
银牌会员9年生产商
关注展位 全部试剂
产品详情

Quantity size:

0.2ml

Concentration:

1mg/ml  三羟基三甲基辅酶A裂解酶抗体 Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

Hydroxymethylglutaryl-CoA lyase (HMGCL) is found in fibroblasts, liver and lymphoblasts. It has a role in ketogenesis and leucine catabolism. Defects in HMGCL are the cause of 3-hydroxy-3-methylglutaryl-CoA lyase deficiency (hydroxymethylglutaricaciduria), 三羟基三甲基辅酶A裂解酶抗体an autosomal recessive disease which can lead to hypoglycemia and coma.

三羟基三甲基辅酶A裂解酶抗体Also known as:

3 hydroxy 3 methylglutaryl CoA lyase; 3 hydroxy 3 methylglutaryl Coenzyme A lyase; 3 hydroxymethyl 3 methylglutaryl Coenzyme A lyase (hydroxymethylglutaricaciduria); 3 hydroxymethyl 3 methylglutaryl Coenzyme A lyase; 3-hydroxy-3-methylglutarate-CoA lyase; HL; HMG CoA lyase; HMG CoA Lyase Deficiency; HMG-CoA lyase; HMGCL; HMGCL_HUMAN; Hydroxymethylglutaricaciduria; Hydroxymethylglutaryl CoA lyase; Hydroxymethylglutaryl 三羟基三甲基辅酶A裂解酶抗体CoA lyase mitochondrial; Hydroxymethylglutaryl-CoA lyase; mitochondrial; MS725; OTTHUMP00000044830.

Specificity:

Rabbit Polyclonal IgG, affinity purified by Protein A.

Reacts with: Human, Mouse, Rat, Chicken, Dog, Horse, Rabbit, .

Immunogen: KLH conjugated synthetic peptide derived from human HMGCL.

三羟基三甲基辅酶A裂解酶抗体Predicted Molecular Weight: 32kDa.

Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

kl395Hu01抑制素A(INHA)多克隆抗体Polyclonal Antibody to Inhibin A (INHA)

kl395Po01抑制素A(INHA)多克隆抗体Polyclonal Antibody to Inhibin A (INHA)

kl395Ra01抑制素A(INHA)多克隆抗体Polyclonal Antibody to Inhibin A (INHA)

kl396Hu01性激素结合球蛋白(SHBG)多克隆抗体Polyclonal Antibody to Sex Hormone Binding Globulin (SHBG)

kl396Mu01性激素结合球蛋白(SHBG)多克隆抗体Polyclonal Antibody to Sex Hormone Binding Globulin (SHBG)

kl396Ra01性激素结合球蛋白(SHBG)多克隆抗体Polyclonal Antibody to Sex Hormone Binding Globulin (SHBG)

kl397Hu01转化生长因子β受体Ⅰ(TGFβR1)多克隆抗体Polyclonal Antibody to Transforming Growth Factor Beta Receptor I (TGFbR1)

kl399Ca01高迁移率族蛋白1(HMG1)多克隆抗体Polyclonal Antibody to High Mobility Group Protein 1 (HMG1)

kl399Hu01高迁移率族蛋白1(HMG1)多克隆抗体Polyclonal Antibody to High Mobility Group Protein 1 (HMG1)

kl399Mu01高迁移率族蛋白1(HMG1)多克隆抗体Polyclonal Antibody to High Mobility Group Protein 1 (HMG1)

kl399Po01高迁移率族蛋白1(HMG1)多克隆抗体Polyclonal Antibody to High Mobility Group Protein 1 (HMG1)

kl399Ra01高迁移率族蛋白1(HMG1)多克隆抗体Polyclonal Antibody to High Mobility Group Protein 1 (HMG1)

kl402Hu01基质金属蛋白酶12(MMP12)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 12 (MMP12)

kl402Mu01基质金属蛋白酶12(MMP12)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 12 (MMP12)

kl402Ra01基质金属蛋白酶12(MMP12)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 12 (MMP12)

kl404Hu01神经颗粒素(NRGN)多克隆抗体Polyclonal Antibody to Neurogranin (NRGN)

kl406Ra01性别决定区Y框蛋白2(SOX2)多克隆抗体Polyclonal Antibody to Sex Determining Region Y Box Protein 2 (SOX2)

kl408Hu01激肽释放酶9(KLK9)多克隆抗体Polyclonal Antibody to Kallikrein 9 (KLK9)

kl408Ra01激肽释放酶9(KLK9)多克隆抗体Polyclonal Antibody to Kallikrein 9 (KLK9)

kl410Hu01GATA结合蛋白3(GATA3)多克隆抗体Polyclonal Antibody to GATA Binding Protein 3 (GATA3)


三羟基三甲基辅酶A裂解酶抗体信息由上海康朗生物科技有限公司为您提供,如您想了解更多关于三羟基三甲基辅酶A裂解酶抗体报价、型号、参数等信息, 欢迎来电或留言咨询。除供应三羟基三甲基辅酶A裂解酶抗体外,上海康朗生物科技有限公司还可为您提供三羟基三甲基辅酶A合成酶2抗体、三羟基三甲基辅酶A合成酶1等产品, 公司有专业的客户服务团队,是您值得信赖的合作伙伴。

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