亨丁顿舞蹈症相互作用蛋白12/HIP1R抗体

参考价:面议
供货周期: 现货
品牌: 康朗生物
规格: 0.1ml/0.2ml
货号: KL9067R
CAS号:
上海康朗生物科技有限公司
银牌会员9年生产商
关注展位 全部试剂
产品详情

Quantity size:

0.2ml

Concentration:

1mg/ml 亨丁顿舞蹈症相互作用蛋白12/HIP1R抗体  Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

Huntington disease is associated with the expansion of a polyglutamine tract, greater than 35 repeats, in the HD gene product, huntingtin. HIP1, a membrane-associated protein, binds specifically to the N-terminus of human huntingtin. HIP1 is ubiquitously expressed in different brain regions at low levels and exhibits nearly identical subcellular fractionation as huntingtin. The HIP1 gene locates to the human chromosome 7q11.23.亨丁顿舞蹈症相互作用蛋白12/HIP1R抗体 The huntingtin-HIP1 interaction is restricted to the brain and is inversely correlated to the polyglutamine length in the huntingtin, suggesting that loss of normal huntingtin-HIP1 interaction may compromise the membrane-cytoskeletal integrity in the brain. HIP1 contains an endocytic multidomain protein with a C-terminal Actin-binding domain, a central coiled-coil forming region and an N-terminal ENTH domain. HIP1 may be involved in vesicle亨丁顿舞蹈症相互作用蛋白12/HIP1R抗体 trafficking; the structural integrity of HIP1 is crucial for maintenance of normal vesicle size in vivo. HIP12 is a non-proapoptotic member of the HIP gene family that is expressed in the brain and shares a similar subcellular distribution pattern with HIP1. However, HIP12 differs from HIP1 in its pattern of expression at both the mRNA and protein level. HIP12 does not directly interact with huntingtin but can interact with HIP1.

亨丁顿舞蹈症相互作用蛋白12/HIP1R抗体Also known as:

Hip1 related; HIP12; HIP3; Huntingtin Interacting Protein 1 Related; HIP1R; Huntingtin interacting protein 12; HIP1R_HUMAN.

Specificity:

Rabbit Polyclonal IgG, affinity purified by Protein A.

Reacts with: Human, Mouse, Rat, Pig, Cow, Horse, .

Immunogen: KLH conjugated synthetic peptide derived from human HIP1R/HI.

Predicted Molecular Weight: 119kDa.

亨丁顿舞蹈症相互作用蛋白12/HIP1R抗体Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  IF=1:50-200   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

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亨丁顿舞蹈症相互作用蛋白12/HIP1R抗体信息由上海康朗生物科技有限公司为您提供,如您想了解更多关于亨丁顿舞蹈症相互作用蛋白12/HIP1R抗体报价、型号、参数等信息, 欢迎来电或留言咨询。除供应亨丁顿舞蹈症相互作用蛋白12/HIP1R抗体外,上海康朗生物科技有限公司还可为您提供舞蹈症相关相互作用蛋白1/雌激素相关受体样蛋白1抗体、舞蹈症相关蛋白40/凝血因子8相关蛋白/第八因子相关蛋白抗体、Anti-HIP1抗体等产品, 公司有专业的客户服务团队,是您值得信赖的合作伙伴。

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