Hib乙酰辅酶A水解酶抗体

Quantity size:

0.2ml

Concentration:

1mg/ml  Hib乙酰辅酶A水解酶抗体 Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localizing to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyzes HIBYL-CoA, a saline catabolite, andHib乙酰辅酶A水解酶抗体 β-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of β-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterized by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.

Hib乙酰辅酶A水解酶抗体Also known as:

3 hydroxyisobutyryl Coenzyme A hydrolase; 3 hydroxyisobutyryl Coenzyme A hydrolase, mitochondrial; 3-hydroxyisobutyryl-CoA hydrolase; 3-hydroxyisobutyryl-coenzyme A hydrolase; BETA HYDROXYISOBUTYRYL COENZYME A HYDROLASE; HIB CoA hydrolase; HIB-CoA hydrolase; HIBCH; HIBCH_HUMAN; HIBCoAHib乙酰辅酶A水解酶抗体 hydrolase; HIBYL CoA H; HIBYL CoAH; HIBYL-CoA-H; HIBYLCoA H; HIBYLCoAH; mitochondrial; HIBCH_HUMAN.

Specificity:

●

Rabbit Polyclonal IgG, affinity purified by Protein A.

●

Reacts with: Human, .

●

Immunogen: KLH conjugated synthetic peptide derived from human HIBCH .

●

Hib乙酰辅酶A水解酶抗体Predicted Molecular Weight: 39kDa.

Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

kl433Mu01蛋白激酶Cδ(PKCδ)多克隆抗体Polyclonal Antibody to Protein Kinase C Delta (PKCd)

kl433Ra01蛋白激酶Cδ(PKCδ)多克隆抗体Polyclonal Antibody to Protein Kinase C Delta (PKCd)

kl932Hu01甘油醛-3-磷酸脱氢酶(GAPDH)多克隆抗体Polyclonal Antibody to Glyceraldehyde-3-Phosphate Dehydrogenase (GAPDH)

kl932Mu01甘油醛-3-磷酸脱氢酶(GAPDH)多克隆抗体Polyclonal Antibody to Glyceraldehyde-3-Phosphate Dehydrogenase (GAPDH)

kl928Hu01肿瘤蛋白p53(TP53)多克隆抗体Polyclonal Antibody to Tumor Protein p53 (TP53)

kl928Mu01肿瘤蛋白p53(TP53)多克隆抗体Polyclonal Antibody to Tumor Protein p53 (TP53)

kl928Ra01肿瘤蛋白p53(TP53)多克隆抗体Polyclonal Antibody to Tumor Protein p53 (TP53)

kl207Hu01谷丙转氨酶(ALT)多克隆抗体Polyclonal Antibody to Alanine Aminotransferase (ALT)

kl207Mu01谷丙转氨酶(ALT)多克隆抗体Polyclonal Antibody to Alanine Aminotransferase (ALT)

kl207Ra01谷丙转氨酶(ALT)多克隆抗体Polyclonal Antibody to Alanine Aminotransferase (ALT)

kl421Hu01髓鞘少突胶质细胞糖蛋白(MOG)多克隆抗体Polyclonal Antibody to Myelin Oligodendrocyte Glycoprotein (MOG)

kl421Mu01髓鞘少突胶质细胞糖蛋白(MOG)多克隆抗体Polyclonal Antibody to Myelin Oligodendrocyte Glycoprotein (MOG)

kl421Ra01髓鞘少突胶质细胞糖蛋白(MOG)多克隆抗体Polyclonal Antibody to Myelin Oligodendrocyte Glycoprotein (MOG)

kl049Hu01干扰素γ(IFNγ)多克隆抗体Polyclonal Antibody to Interferon Gamma (IFNg)

kl049Mu01干扰素γ(IFNγ)多克隆抗体Polyclonal Antibody to Interferon Gamma (IFNg)

kl049Ra01干扰素γ(IFNγ)多克隆抗体Polyclonal Antibody to Interferon Gamma (IFNg)

kl146Hu01血管内皮生长因子D(VEGFD)多克隆抗体Polyclonal Antibody to Vascular Endothelial Growth Factor D (VEGFD)

kl146Mu01血管内皮生长因子D(VEGFD)多克隆抗体Polyclonal Antibody to Vascular Endothelial Growth Factor D (VEGFD)

kl146Ra01血管内皮生长因子D(VEGFD)多克隆抗体Polyclonal Antibody to Vascular Endothelial Growth Factor D (VEGFD)

kl145Hu01血管内皮生长因子C(VEGFC)多克隆抗体Polyclonal Antibody to Vascular Endothelial Growth Factor C (VEGFC)

kl145Mu01血管内皮生长因子C(VEGFC)多克隆抗体Polyclonal Antibody to Vascular Endothelial Growth Factor C (VEGFC)

kl145Ra01血管内皮生长因子C(VEGFC)多克隆抗体Polyclonal Antibody to Vascular Endothelial Growth Factor C (VEGFC)

kl144Hu01血管内皮生长因子B(VEGFB)多克隆抗体Polyclonal Antibody to Vascular Endothelial Growth Factor B (VEGFB)