供货周期: | 现货 |
品牌: | 康朗生物 |
规格: | 0.1ml/0.2ml |
货号: | KL16501R |
CAS号: |
Quantity size:
0.2ml
Concentration:
1mg/ml 跨膜蛋白76/TMEM76抗体 Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
This gene encodes a lysosomal acetyltransferase, which is one of several enzymes involved in the lysosomal degradation of heparin sulfate. Mutations in this gene are associated with Sanfilippo跨膜蛋白76/TMEM76抗体 syndrome C, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. [provided by RefSeq, Jan 2009]
跨膜蛋白76/TMEM76抗体Also known as:
Heparan-alpha-glucosaminide N-acetyltransferase; HGNAT_HUMAN; HGSNAT; TMEM76; Transmembrane protein 76.
Specificity:
●
Rabbit Polyclonal IgG,跨膜蛋白76/TMEM76抗体 affinity purified by Protein A.
●
Reacts with: Human, Mouse, Dog, Rabbit, .
●
Immunogen: KLH conjugated synthetic peptide derived from human HGSNAT.
●
跨膜蛋白76/TMEM76抗体Predicted Molecular Weight: 73kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
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