供货周期: | 现货 |
品牌: | 康朗生物 |
规格: | 0.1ml/0.2ml |
货号: | KL15542R |
CAS号: |
Quantity size:
0.2ml
Concentration:
1mg/ml α-L-艾杜糖苷酶抗体 Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for theα-L-艾杜糖苷酶抗体 lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I). [provided by RefSeq, Jul 2008].
α-L-艾杜糖苷酶抗体Also known as:
IDUA_HUMAN; Alpha-L-iduronidase; IDA; Iduronidase alpha L; MPS1.
Specificity:
●
Rabbit Polyclonal IgG,α-L-艾杜糖苷酶抗体 affinity purified by Protein A.
●
Reacts with: Human, Mouse, Rat, Horse, .
●
Immunogen: KLH conjugated synthetic peptide derived from human IDUA.
●
α-L-艾杜糖苷酶抗体Predicted Molecular Weight: 70kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
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