供货周期: | 现货 |
品牌: | 康朗生物 |
规格: | 0.1ml/0.2ml |
货号: | KL19177R |
CAS号: |
Quantity size:
0.2ml
Concentration:
1mg/ml Myoferlin抗体 Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Mutations in dysferlin, a protein associated with the plasma membrane, can cause muscle weakness that affects both proximal and distal muscles. The protein encoded by this gene is a type II membrane protein that is structurally similar to dysferlin. It is a member of the Myoferlin抗体ferlin family and associates with both plasma and nuclear membranes. The protein contains C2 domains that play a role in calcium-mediated membrane fusion events, suggesting that it may be involved in membrane regeneration and repair. Two transcript variants encoding different isoforms have been found for this gene. Other possible variants have been detected, but their full-length nature has not been determined. [provided by RefSeq, Dec 2008]
Myoferlin抗体Also known as:
Myoferlin; MYOF_HUMAN; Fer-1-like protein 3.
Specificity:
●
Rabbit Polyclonal IgG,Myoferlin抗体 affinity purified by Protein A.
●
Reacts with: Human, Mouse, Rat, Dog, Horse, .
●
Immunogen: KLH conjugated synthetic peptide derived from human Myoferlin.
●
Myoferlin抗体Predicted Molecular Weight: 234kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
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