供货周期: | 现货 |
品牌: | 康朗生物 |
规格: | 0.1ml/0.2ml |
货号: | KL19002R |
CAS号: |
Quantity size:
0.2ml
Concentration:
1mg/ml N-乙酰基-α葡萄糖苷酶抗体 Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
This gene encodes an enzyme that degrades heparan sulfate by hydrolysis of terminal N-acetyl-D-glucosamine residues in N-acetyl-alpha-D-glucosaminides. Defects in this gene are the cause of N-乙酰基-α葡萄糖苷酶抗体mucopolysaccharidosis type IIIB (MPS-IIIB), also known as Sanfilippo syndrome B. This disease is characterized by the lysosomal accumulation and urinary excretion of heparan sulfate. [provided by RefSeq, Jul 2008]
N-乙酰基-α葡萄糖苷酶抗体Also known as:
Alpha N acetylglucosaminidase; alpha N acetylglucosaminidase, lysosomal; Alpha-N-acetylglucosaminidase 77 kDa form; ANAG; ANAG_HUMAN; MPS IIIB; MPS3B; N acetyl alpha glucosaminidase; N acetylglucosaminidase, alpha; N-acetyl-alpha-glucosaminidase; NAG; NAGLU; UFHSD 1; UFHSD; UFHSD1.
Specificity:
●
Rabbit Polyclonal IgG,N-乙酰基-α葡萄糖苷酶抗体 affinity purified by Protein A.
●
Reacts with: Human, Mouse, Dog, Pig, Horse, Rabbit, Sheep, .
●
Immunogen: KLH conjugated synthetic peptide derived from human NAGLU.
●
Predicted Molecular Weight: 80kDa.
N-乙酰基-α葡萄糖苷酶抗体Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
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