神经氨酸酶1抗体

参考价:面议
供货周期: 现货
品牌: 康朗生物
规格: 0.1ml/0.2ml
货号: KL8624R
CAS号:
上海康朗生物科技有限公司
银牌会员9年生产商
关注展位 全部试剂
产品详情

Quantity size:

0.2ml

Concentration:

1mg/ml 神经氨酸酶1抗体  Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

The protein encoded by this gene is a lysosomal enzyme that cleaves terminal sialic acid residues from substrates such as glycoproteins and glycolipids. In the lysosome, this enzyme is part of a heterotrimeric complex together with beta-galactosidase and cathepsin A (the latter is also referred to as 'protective protein'). Mutations in this gene 神经氨酸酶1抗体can lead to sialidosis, a lysosomal storage disease that can be type 1 (cherry red spot-myoclonus syndrome or normosomatic type), which is late-onset, or type 2 (the dysmorphic type), which occurs at an earlier age with increased severity. [provided by RefSeq, Jul 2008]

神经氨酸酶1抗体Also known as:

Acetylneuraminyl hydrolase; exo-alpha-sialidase; G9 sialidase; Lysosomal sialidase; N acetyl alpha neuraminidase 1; N-acetyl-alpha-neuraminidase 1; NANH; NEU; NEU1; NEUR1_HUMAN; Neuraminidase 1; Neuraminidase; SIAL1; sialidase 1 (lysosomal sialidase); Sialidase 1; Sialidase, lysosomal; Sialidase-1.

Specificity:

Rabbit Polyclonal IgG,神经氨酸酶1抗体 affinity purified by Protein A.

Reacts with: Human, Rat, Cow, .

Immunogen: KLH conjugated synthetic peptide derived from human NEU1/Neuraminidase.

神经氨酸酶1抗体Predicted Molecular Weight: 45kDa.

Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

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kl543Ra01免疫球蛋白M(IgM)多克隆抗体Polyclonal Antibody to Immunoglobulin M (IgM)

kl543Bo01免疫球蛋白M(IgM)多克隆抗体Polyclonal Antibody to Immunoglobulin M (IgM)

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kl544Bo01免疫球蛋白G(IgG)多克隆抗体Polyclonal Antibody to Immunoglobulin G (IgG)

kl544Po01免疫球蛋白G(IgG)多克隆抗体Polyclonal Antibody to Immunoglobulin G (IgG)


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