骨硬化病相关跨膜蛋白1抗体

Quantity size:

0.2ml

Concentration:

1mg/ml 骨硬化病相关跨膜蛋白1抗体  Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

OSTM1 (osteopetrosis associated transmembrane protein 1), also known as gl (gray-lethal) or HSPC019, is a 338 amino acid single-pass type I membrane protein that is expressed primarily in osteoclasts and melanocytes as well as brain, kidney and spleen. Bone autosomal recessive osteopetrosis (ARO) is the most severe form of hereditary bone disease whose 骨硬化病相关跨膜蛋白1抗体cellular basis is in the osteoclast and is characterized by abnormally dense bone, due to defective resorption of immature bone. ARO is suggested to be caused by mutations in the OSTM1 gene. The disorder occurs in two forms: a severe autosomal recessive form occurring in utero, infancy, or childhood, and a benign autosomal dominant form occurring in adolescence骨硬化病相关跨膜蛋白1抗体 or adulthood. Defects in the OSTM1 gene are also the cause of the spontaneous gl mutant, which is responsible for a coat color defect in mice.

骨硬化病相关跨膜蛋白1抗体Also known as:

GAIP-interacting protein N terminus; GIPN; GL antibody Grey lethal osteopetrosis; HSPC019; OPTB5; Osteopetrosis-associated transmembrane protein 1; Ostm1; OSTM1_HUMAN.

Specificity:

●

Rabbit Polyclonal IgG, affinity purified by Protein A.

●

Reacts with: Human, Mouse, Rat, Pig, .

●

Immunogen: KLH conjugated synthetic peptide derived from human OSTM1.

●

骨硬化病相关跨膜蛋白1抗体Predicted Molecular Weight: 33kDa.

Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  Flow-Cyt=1:20-300  IF=1:50-200   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

kl675Ra01凝血因子Ⅴ(F5)多克隆抗体Polyclonal Antibody to Coagulation Factor V (F5)

kl677Hu01凝血因子Ⅻ(F12)多克隆抗体Polyclonal Antibody to Coagulation Factor XII (F12)

kl677Mu01凝血因子Ⅻ(F12)多克隆抗体Polyclonal Antibody to Coagulation Factor XII (F12)

kl680Hu01棕榈酰化膜蛋白2(MPP2)多克隆抗体Polyclonal Antibody to Membrane Protein, klmitoylated 2 (MPP2)

kl680Ra01棕榈酰化膜蛋白2(MPP2)多克隆抗体Polyclonal Antibody to Membrane Protein, klmitoylated 2 (MPP2)

kl681Hu01乙醇脱氢酶1(ADH1)多克隆抗体Polyclonal Antibody to Alcohol Dehydrogenase 1 (ADH1)

kl681Mu01乙醇脱氢酶1(ADH1)多克隆抗体Polyclonal Antibody to Alcohol Dehydrogenase 1 (ADH1)

kl681Ra01乙醇脱氢酶1(ADH1)多克隆抗体Polyclonal Antibody to Alcohol Dehydrogenase 1 (ADH1)

kl683Hu01Toll样受体6(TLR6)多克隆抗体Polyclonal Antibody to Toll Like Receptor 6 (TLR6)

kl685Hu01CD14分子(CD14)多克隆抗体Polyclonal Antibody to Cluster Of Differentiation 14 (CD14)

kl685Ra01CD14分子(CD14)多克隆抗体Polyclonal Antibody to Cluster Of Differentiation 14 (CD14)

kl687Hu01钙结合蛋白(CR)多克隆抗体Polyclonal Antibody to Calretinin (CR)

kl688Hu01TGFβ诱导早期应答基因1(TIEG1)多克隆抗体Polyclonal Antibody to TGF Beta Inducible Early Response Gene 1 (TIEG1)

kl690Hu01激肽释放酶8(KLK8)多克隆抗体Polyclonal Antibody to Kallikrein 8 (KLK8)

kl691Hu01激肽释放酶6(KLK6)多克隆抗体Polyclonal Antibody to Kallikrein 6 (KLK6)

kl691Ra01激肽释放酶6(KLK6)多克隆抗体Polyclonal Antibody to Kallikrein 6 (KLK6)

kl692Hu01神经纤维网蛋白1(NRP1)多克隆抗体Polyclonal Antibody to Neuropilin 1 (NRP1)

kl692Mu01神经纤维网蛋白1(NRP1)多克隆抗体Polyclonal Antibody to Neuropilin 1 (NRP1)

kl692Ra01神经纤维网蛋白1(NRP1)多克隆抗体Polyclonal Antibody to Neuropilin 1 (NRP1)