过氧化物酶体生成蛋白7抗体

参考价:面议
供货周期: 现货
品牌: 康朗生物
规格: 0.1ml/0.2ml
货号: KL19913R
CAS号:
上海康朗生物科技有限公司
银牌会员9年生产商
关注展位 全部试剂
产品详情

Quantity size:

0.2ml

Concentration:

1mg/ml 过氧化物酶体生成蛋白7抗体  Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

This gene encodes the cytosolic receptor for the set of peroxisomal matrix enzymes targeted to the organelle by the peroxisome targeting signal 2 (PTS2). Defects in this gene cause peroxisome biogenesis disorders (PBDs), which are characterized by multiple defects in peroxisome function. There are at least 14 complementation groups for PBDs, with more than过氧化物酶体生成蛋白7抗体 one phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene have been associated with PBD complementation group 11 (PBD-CG11) disorders, rhizomelic chondrodysplasia punctata type 1 (RCDP1), and Refsum disease (RD). [provided by RefSeq, Oct 2008]

过氧化物酶体生成蛋白7抗体Also known as:

PBD9B; PCDP1; Peroxin 7; Peroxin-7; Peroxisomal PTS2 receptor; Peroxisomal targeting signal 2 receptor; Peroxisome biogenesis factor 7; Peroxisome targeting signal 2 receptor; PEX7; PEX7 protein; PEX7_HUMAN; PTS2 receptor; PTS2R; RCDP1; RD.

Specificity:

Rabbit Polyclonal IgG, 过氧化物酶体生成蛋白7抗体affinity purified by Protein A.

Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Horse, Rabbit, Sheep, .

Immunogen: KLH conjugated synthetic peptide derived from human PEX7.

过氧化物酶体生成蛋白7抗体Predicted Molecular Weight: 36kDa.

Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

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过氧化物酶体生成蛋白7抗体信息由上海康朗生物科技有限公司为您提供,如您想了解更多关于过氧化物酶体生成蛋白7抗体报价、型号、参数等信息, 欢迎来电或留言咨询。除供应过氧化物酶体生成蛋白7抗体外,上海康朗生物科技有限公司还可为您提供成蛋白相关蛋白1抗体、过氧化物酶体增殖物激活受体γ(PPARγ)重组蛋白 等产品, 公司有专业的客户服务团队,是您值得信赖的合作伙伴。

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