过氧化物酶体生物合成因子19抗体

参考价:面议
供货周期: 现货
品牌: 康朗生物
规格: 0.1ml/0.2ml
货号: KL12623R
CAS号:
上海康朗生物科技有限公司
银牌会员9年生产商
关注展位 全部试剂
产品详情

Quantity size:

0.2ml

Concentration:

1mg/ml 过氧化物酶体生物合成因子19抗体  Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

This gene is necessary for early peroxisomal biogenesis. It acts both as a cytosolic chaperone and as an import receptor for peroxisomal membrane proteins (PMPs). Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome 过氧化物酶体生物合成因子19抗体function. These disorders have at least 14 complementation groups, with more than one phenotype being observed for some complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of 过氧化物酶体生物合成因子19抗体Zellweger syndrome (ZWS), as well as peroxisome biogenesis disorder complementation group 14 (PBD-CG14), which is also known as PBD-CGJ. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Aug 2010]

Also known as:

33 kDa housekeeping protein; D1S2223E; HK33; Housekeeping gene 33kD; OK/SW-cl.22; PBD12A; Peroxin 19; Peroxin-19; Peroxisomal biogenesis factor 19; Peroxisomal farnesylated protein; PEX19;过氧化物酶体生物合成因子19抗体 PEX19_HUMAN; PMP1; PMPI; PXF; PXMP1.

Specificity:

Rabbit Polyclonal IgG, affinity purified by Protein A.

Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Horse, .

Immunogen: KLH conjugated synthetic peptide derived from human PEX19.

过氧化物酶体生物合成因子19抗体Predicted Molecular Weight: 33kDa.

Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

kl225Eq01心钠肽(ANP)多克隆抗体Polyclonal Antibody to Atrial Natriuretic Peptide (ANP)

kl225Gu01心钠肽(ANP)多克隆抗体Polyclonal Antibody to Atrial Natriuretic Peptide (ANP)

kl225Mu01心钠肽(ANP)多克隆抗体Polyclonal Antibody to Atrial Natriuretic Peptide (ANP)

kl225Po01心钠肽(ANP)多克隆抗体Polyclonal Antibody to Atrial Natriuretic Peptide (ANP)

kl225Rb51心钠肽(ANP)多克隆抗体Polyclonal Antibody to Atrial Natriuretic Peptide (ANP)

kl227Bo01亲环素B(CYPB)多克隆抗体Polyclonal Antibody to Cyclophilin B (CYPB)

kl227Ga01亲环素B(CYPB)多克隆抗体Polyclonal Antibody to Cyclophilin B (CYPB)

kl227Hu01亲环素B(CYPB)多克隆抗体Polyclonal Antibody to Cyclophilin B (CYPB)

kl227Mu01亲环素B(CYPB)多克隆抗体Polyclonal Antibody to Cyclophilin B (CYPB)

kl227Ra01亲环素B(CYPB)多克隆抗体Polyclonal Antibody to Cyclophilin B (CYPB)

kl227Rb51亲环素B(CYPB)多克隆抗体Polyclonal Antibody to Cyclophilin B (CYPB)

kl228Ga01抗缪勒管激素(AMH)多克隆抗体Polyclonal Antibody to Anti-Mullerian Hormone (AMH)

kl228Hu01抗缪勒管激素(AMH)多克隆抗体Polyclonal Antibody to Anti-Mullerian Hormone (AMH)

kl228Mu01抗缪勒管激素(AMH)多克隆抗体Polyclonal Antibody to Anti-Mullerian Hormone (AMH)

kl228Po01抗缪勒管激素(AMH)多克隆抗体Polyclonal Antibody to Anti-Mullerian Hormone (AMH)

kl228Ra01抗缪勒管激素(AMH)多克隆抗体Polyclonal Antibody to Anti-Mullerian Hormone (AMH)

kl229Hu01白介素2受体β(IL2Rβ)多克隆抗体Polyclonal Antibody to Interleukin 2 Receptor Beta (IL2Rb)

kl229Mu01白介素2受体β(IL2Rβ)多克隆抗体Polyclonal Antibody to Interleukin 2 Receptor Beta (IL2Rb)

kl229Ra01白介素2受体β(IL2Rβ)多克隆抗体Polyclonal Antibody to Interleukin 2 Receptor Beta (IL2Rb)

kl229Si01白介素2受体β(IL2Rβ)多克隆抗体Polyclonal Antibody to Interleukin 2 Receptor Beta (IL2Rb)

kl230Hu01丝氨酸蛋白酶1(PRSS1)多克隆抗体Polyclonal Antibody to Protease, Serine 1 (PRSS1)

kl230Ra01丝氨酸蛋白酶1(PRSS1)多克隆抗体Polyclonal Antibody to Protease, Serine 1 (PRSS1)

kl231Cp01尿皮质素1(UCN1)多克隆抗体Polyclonal Antibody to Urocortin 1 (UCN1)


过氧化物酶体生物合成因子19抗体信息由上海康朗生物科技有限公司为您提供,如您想了解更多关于过氧化物酶体生物合成因子19抗体报价、型号、参数等信息, 欢迎来电或留言咨询。除供应过氧化物酶体生物合成因子19抗体外,上海康朗生物科技有限公司还可为您提供过氧化物酶体增殖物激活受体γ(PPARγ)重组蛋白 、人过氧化物酶体增殖物激活受体δ检测试剂盒等产品, 公司有专业的客户服务团队,是您值得信赖的合作伙伴。

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