过氧化物酶体生物合成因子5抗体

Quantity size:

0.2ml

Concentration:

1mg/ml 过氧化物酶体生物合成因子5抗体  Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

The product of this gene binds to the C-terminal PTS1-type tripeptide peroxisomal targeting signal (SKL-type) and plays an essential role in peroxisomal protein import. Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome 过氧化物酶体生物合成因子5抗体function. The peroxisomal biogenesis disorders are a heterogeneous group with at least 14 complementation groups and with more than 1 phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of过氧化物酶体生物合成因子5抗体 neonatal adrenoleukodystrophy (NALD), a cause of Zellweger syndrome (ZWS) as well as may be a cause of infantile Refsum disease (IRD). Alternatively spliced transcript variants encoding different isoforms have been identified. [provided by RefSeq, Oct 2008]

Also known as:

FLJ50634; FLJ50721; FLJ51948; Peroxin 5; Peroxin-5; Peroxisomal biogenesis factor 5; Peroxisomal C terminal过氧化物酶体生物合成因子5抗体 targeting signal import receptor; Peroxisomal C-terminal targeting signal import receptor; Peroxisomal targeting signal 1 receptor; Peroxisome receptor 1; pex5; PEX5_HUMAN; PTS1 BP; PTS1 receptor; PTS1-BP; PTS1R; PXR1.

Specificity:

●

Rabbit Polyclonal IgG, affinity purified by Protein A.

●

Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Horse, Sheep, .

●

Immunogen: KLH conjugated synthetic peptide derived from human PEX5.

●

过氧化物酶体生物合成因子5抗体Predicted Molecular Weight: 71kDa.

Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

kl231Hu01尿皮质素1(UCN1)多克隆抗体Polyclonal Antibody to Urocortin 1 (UCN1)

kl231Mu01尿皮质素1(UCN1)多克隆抗体Polyclonal Antibody to Urocortin 1 (UCN1)

kl231Ra01尿皮质素1(UCN1)多克隆抗体Polyclonal Antibody to Urocortin 1 (UCN1)

kl233Bo01蛋白激酶Cη(PKCη)多克隆抗体Polyclonal Antibody to Protein Kinase C Eta (PKCh)

kl233Hu01蛋白激酶Cη(PKCη)多克隆抗体Polyclonal Antibody to Protein Kinase C Eta (PKCh)

kl233Mu01蛋白激酶Cη(PKCη)多克隆抗体Polyclonal Antibody to Protein Kinase C Eta (PKCh)

kl233Ra01蛋白激酶Cη(PKCη)多克隆抗体Polyclonal Antibody to Protein Kinase C Eta (PKCh)

kl234Hu01免疫球蛋白G4(IgG4)多克隆抗体Polyclonal Antibody to Immunoglobulin G4 (IgG4)

kl235Hu01补体1抑制因子(C1INH)多克隆抗体Polyclonal Antibody to Complement 1 Inhibitor (C1INH)

kl235Mu01补体1抑制因子(C1INH)多克隆抗体Polyclonal Antibody to Complement 1 Inhibitor (C1INH)

kl235Ra01补体1抑制因子(C1INH)多克隆抗体Polyclonal Antibody to Complement 1 Inhibitor (C1INH)

kl235Rb51补体1抑制因子(C1INH)多克隆抗体Polyclonal Antibody to Complement 1 Inhibitor (C1INH)

kl238Hu01酪氨酸酶(TYR)多克隆抗体Polyclonal Antibody to Tyrosinase (TYR)

kl238Ra01酪氨酸酶(TYR)多克隆抗体Polyclonal Antibody to Tyrosinase (TYR)

kl243Hu01对氧磷酶1(PON1)多克隆抗体Polyclonal Antibody to klaoxonase 1 (PON1)

kl243Mu01对氧磷酶1(PON1)多克隆抗体Polyclonal Antibody to klaoxonase 1 (PON1)

kl243Ra01对氧磷酶1(PON1)多克隆抗体Polyclonal Antibody to klaoxonase 1 (PON1)

kl244Hu01胱天蛋白酶2(CASP2)多克隆抗体Polyclonal Antibody to Caskle 2 (CASP2)

kl249Hu01Nischarin蛋白(NISCH)多克隆抗体Polyclonal Antibody to Nischarin (NISCH)

kl252Bo01载脂蛋白C1(APOC1)多克隆抗体Polyclonal Antibody to Apolipoprotein C1 (APOC1)

kl252Ca01载脂蛋白C1(APOC1)多克隆抗体Polyclonal Antibody to Apolipoprotein C1 (APOC1)

kl252Hu01载脂蛋白C1(APOC1)多克隆抗体Polyclonal Antibody to Apolipoprotein C1 (APOC1)

kl252Mu01载脂蛋白C1(APOC1)多克隆抗体Polyclonal Antibody to Apolipoprotein C1 (APOC1)