供货周期: | 现货 |
品牌: | 康朗生物 |
规格: | 0.1ml/0.2ml |
货号: | KL9589R |
CAS号: |
Quantity size:
0.2ml
Concentration:
1mg/ml 跨膜蛋白43抗体 Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
This gene belongs to the TMEM43 family. Defects in this gene are the cause of familial arrhythmogenic right ventricular dysplasia type 5 (ARVD5), also known as arrhythmogenic right ventricular cardiomyopathy type 5 (ARVC5). Arrhythmogenic right ventricular dysplasia is an inheri跨膜蛋白43抗体ted disorder, often involving both ventricles, and is characterized by ventricular tachycardia, heart failure, sudden cardiac跨膜蛋白43抗体 death, and fibrofatty replacement of cardiomyocytes. This gene contains a response element for PPAR gamma (an adipogenic transcription factor), which may explain the fibrofatty replacement of the myocardium, a characteristic pathological finding in ARVC. [provided by RefSeq, Oct 2008]
Also known as:
跨膜蛋白43抗体ARVC5; ARVD5; EDMD7; LUMA; Protein LUMA; Tmem43; TMM43_HUMAN; Transmembrane protein 43,
Specificity:
●
Rabbit Polyclonal IgG, affinity purified by Protein A.
●
Reacts with: Human, Mouse, Rat, .
●
跨膜蛋白43抗体Immunogen: KLH conjugated synthetic peptide derived from human TMEM43.
●
Predicted Molecular Weight: 45kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
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